Literature DB >> 19319631

Portal hypertension resulted from paroxysmal nocturnal hemoglobinuria: a case report and review of literature.

Da-Long Yin1, Lian-Xin Liu2, Shu-Geng Zhang1, Lan-Tian Tian1, Zhao-Yang Lu1, Hong-Chi Jiang1.   

Abstract

Paroxysmal nocturnal hemoglobinuria is a rare intravascular hemolytic anemia, and thrombosis is the leading cause of mortality rate. The hepatic veins is the common site where Budd-Chiari syndrome usually occurs. We confronted a patient who simultaneously happened to have portal vein and superior mesenteric vein thrombosis leading to prehepatic portal hypertension and upper gastrointestinal bleeding. Percutaneous thrombolysis is an efficacious treatment.

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Year:  2009        PMID: 19319631     DOI: 10.1007/s12185-009-0287-4

Source DB:  PubMed          Journal:  Int J Hematol        ISSN: 0925-5710            Impact factor:   2.490


  17 in total

Review 1.  [Treatment of paroxysmal nocturnal hemoglobinuria (PNH)].

Authors:  L Chrobák; P Dulícek; P Zák
Journal:  Vnitr Lek       Date:  2001-12

2.  The complement inhibitor eculizumab in paroxysmal nocturnal hemoglobinuria.

Authors:  Peter Hillmen; Neal S Young; Jörg Schubert; Robert A Brodsky; Gerard Socié; Petra Muus; Alexander Röth; Jeffrey Szer; Modupe O Elebute; Ryotaro Nakamura; Paul Browne; Antonio M Risitano; Anita Hill; Hubert Schrezenmeier; Chieh-Lin Fu; Jaroslaw Maciejewski; Scott A Rollins; Christopher F Mojcik; Russell P Rother; Lucio Luzzatto
Journal:  N Engl J Med       Date:  2006-09-21       Impact factor: 91.245

3.  Combined mechanical and pharmacologic thrombolysis for portal vein thrombosis in liver-graft recipients and in candidates for liver transplantation.

Authors:  Cristina Rossi; Andrea Zambruni; Fabio Ansaloni; Andrea Casadei; Cristina Morelli; Mauro Bernardi; Franco Trevisani
Journal:  Transplantation       Date:  2004-09-27       Impact factor: 4.939

Review 4.  Thrombosis in paroxysmal nocturnal hemoglobinuria at a glance: a clinical review.

Authors:  Panayiotis D Ziakas; Loukia S Poulou; Anastasia Pomoni
Journal:  Curr Vasc Pharmacol       Date:  2008-10       Impact factor: 2.719

5.  Impact of magnetic resonance imaging on the diagnosis of abdominal complications of paroxysmal nocturnal hemoglobinuria.

Authors:  D Mathieu; A Rahmouni; P Villeneuve; M C Anglade; H Rochant; N Vasile
Journal:  Blood       Date:  1995-06-01       Impact factor: 22.113

6.  Splenectomy for massive splenic infarction unmasks paroxysmal nocturnal hemoglobinuria.

Authors:  Costas Tsatalas; Dimitris Margaritis; Despina Pantelidou; Ioannis Kotsianidis; Anastasios J Karayiannakis; Emanuel Spanoudakis; Zafiris Kartasis; Vasiliki Kaloutsi; Alexandros Polychronidis; Ioannis Manavis; George Bourikas
Journal:  Acta Haematol       Date:  2003       Impact factor: 2.195

7.  FDA report: eculizumab (Soliris) for the treatment of patients with paroxysmal nocturnal hemoglobinuria.

Authors:  Andrew Dmytrijuk; Kathy Robie-Suh; Martin H Cohen; Dwaine Rieves; Karen Weiss; Richard Pazdur
Journal:  Oncologist       Date:  2008-09-10

Review 8.  Recent insights into the pathophysiology of paroxysmal nocturnal hemoglobinuria.

Authors:  John Meletis; Evangelos Terpos
Journal:  Med Sci Monit       Date:  2003-07

9.  Superior sagittal sinus thrombosis and Budd-Chiari syndrome due to paroxysmal nocturnal hemoglobinuria managed with transjugular intrahepatic portosystemic shunt: a case report.

Authors:  Abhinav Sharma; Srivenu Itha; Sanjay S Baijal; Ritu Gupta; Atul Sonkar; Rakesh Aggarwal
Journal:  Trop Gastroenterol       Date:  2005 Jul-Sep

10.  Catheter-directed thrombolysis and thrombectomy for the Budd-Chiari syndrome in paroxysmal nocturnal hemoglobinuria in three patients.

Authors:  George P Kuo; Robert A Brodsky; Hyun S Kim
Journal:  J Vasc Interv Radiol       Date:  2006-02       Impact factor: 3.464

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  1 in total

Review 1.  Thrombolytic therapy is effective in paroxysmal nocturnal hemoglobinuria: a series of nine patients and a review of the literature.

Authors:  David J Araten; Rosario Notaro; Howard T Thaler; Nancy Kernan; Farid Boulad; Hugo Castro-Malaspina; Trudy Small; Andromachi Scaradavou; Heather Magnan; Susan Prockop; Sara Chaffee; Jason Gonsky; Raymond Thertulien; Roberto Tarquini; Lucio Luzzatto
Journal:  Haematologica       Date:  2011-12-01       Impact factor: 9.941

  1 in total

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