| Literature DB >> 19302875 |
Jose Carlos Fraga1, Haney O S Gabra, Emmeline E Calkoen, Clare A McLaren, Derek J Roebuck, Martin J Elliott.
Abstract
Long segment congenital tracheal stenosis (LSCTS), associated with complete tracheal rings, is a rare condition, difficult to manage and historically associated with high mortality rate. We report two pairs of identical twins all affected by LSCTS successfully treated by sliding tracheoplasty. All had severe respiratory distress. Three infants had left pulmonary artery (LPA) sling and one intra-cardiac malformation. Slide tracheoplasty was done under cardiopulmonary bypass, and cardiovascular malformations were corrected at the same time. One child needed plication of paralyzed right hemi-diaphragm and another distal tracheal Palmaz stent insertion due severe tracheobronchomalacia. All children are doing well during 6 months follow-up. Slide tracheoplasty seems to produce the same good early results in twins as for singletons with LSCTS.Entities:
Mesh:
Year: 2009 PMID: 19302875 DOI: 10.1016/j.jpedsurg.2008.10.105
Source DB: PubMed Journal: J Pediatr Surg ISSN: 0022-3468 Impact factor: 2.545