Literature DB >> 19302875

Long segment congenital tracheal stenosis in twins successfully treated by slide tracheoplasty.

Jose Carlos Fraga1, Haney O S Gabra, Emmeline E Calkoen, Clare A McLaren, Derek J Roebuck, Martin J Elliott.   

Abstract

Long segment congenital tracheal stenosis (LSCTS), associated with complete tracheal rings, is a rare condition, difficult to manage and historically associated with high mortality rate. We report two pairs of identical twins all affected by LSCTS successfully treated by sliding tracheoplasty. All had severe respiratory distress. Three infants had left pulmonary artery (LPA) sling and one intra-cardiac malformation. Slide tracheoplasty was done under cardiopulmonary bypass, and cardiovascular malformations were corrected at the same time. One child needed plication of paralyzed right hemi-diaphragm and another distal tracheal Palmaz stent insertion due severe tracheobronchomalacia. All children are doing well during 6 months follow-up. Slide tracheoplasty seems to produce the same good early results in twins as for singletons with LSCTS.

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Year:  2009        PMID: 19302875     DOI: 10.1016/j.jpedsurg.2008.10.105

Source DB:  PubMed          Journal:  J Pediatr Surg        ISSN: 0022-3468            Impact factor:   2.545


  2 in total

1.  Histological features of complete tracheal rings in congenital tracheal stenosis.

Authors:  Yuki Fujieda; Keiichi Morita; Hiroaki Fukuzawa; Kosaku Maeda
Journal:  Pediatr Surg Int       Date:  2021-01-02       Impact factor: 1.827

2.  Complete Tracheal Ring Deformity. A Translational Genomics Approach to Pathogenesis.

Authors:  Debora I Sinner; Brenna Carey; Daniela Zgherea; K M Kaufman; Lauren Leesman; Robert E Wood; Michael J Rutter; Alessandro de Alarcon; Ravindhra G Elluru; John B Harley; Jeffrey A Whitsett; Bruce C Trapnell
Journal:  Am J Respir Crit Care Med       Date:  2019-11-15       Impact factor: 21.405

  2 in total

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