CONCLUSION: Preoperative CT and MRI assessment of children with severe or profound sensorineural hearing loss (SNHL) is critical for determining implant candidacy. OBJECTIVES: There are a significant number of children who do not show any auditory development with a cochlear implant (CI), possibly due to cochlear nerve (CN) aplasia/hypoplasia. Regardless of the suspected etiology, if a CI is not providing auditory development the clinician should carefully evaluate the possibility of a CN malformation and re-evaluate the child with detailed neuroimaging studies. If the imaging evaluation shows severe cochlear malformation or CN aplasia there is some developmental urgency to consider auditory brainstem implant (ABI) surgery. SUBJECTS AND METHODS: Twenty-eight children affected by congenital SNHL were examined by CT and MRI. Evaluation of the cerebellopontine angle (CPA), internal auditory canal (IAC), cranial nerves, and membranous labyrinth was performed. Six children had been previously fitted elsewhere with a CI with no sound detection. RESULTS: Suspected congenital anomalies were confirmed by CT and MRI in all 28 children: 16 with associated labyrinthine malformations; 1 with outer, middle, and inner ear malformations; and 2 with associated monolateral facial nerve aplasia.
CONCLUSION: Preoperative CT and MRI assessment of children with severe or profound sensorineural hearing loss (SNHL) is critical for determining implant candidacy. OBJECTIVES: There are a significant number of children who do not show any auditory development with a cochlear implant (CI), possibly due to cochlear nerve (CN) aplasia/hypoplasia. Regardless of the suspected etiology, if a CI is not providing auditory development the clinician should carefully evaluate the possibility of a CN malformation and re-evaluate the child with detailed neuroimaging studies. If the imaging evaluation shows severe cochlear malformation or CN aplasia there is some developmental urgency to consider auditory brainstem implant (ABI) surgery. SUBJECTS AND METHODS: Twenty-eight children affected by congenital SNHL were examined by CT and MRI. Evaluation of the cerebellopontine angle (CPA), internal auditory canal (IAC), cranial nerves, and membranous labyrinth was performed. Six children had been previously fitted elsewhere with a CI with no sound detection. RESULTS: Suspected congenital anomalies were confirmed by CT and MRI in all 28 children: 16 with associated labyrinthine malformations; 1 with outer, middle, and inner ear malformations; and 2 with associated monolateral facial nerve aplasia.
Authors: M Barillari; R Cerini; M Carner; C Cacciatori; F Spagnolli; N Cardobi; M Mandalà; L Colletti; V Colletti; R Pozzi Mucelli Journal: Radiol Med Date: 2011-11-17 Impact factor: 3.469
Authors: Vítor Yamashiro Rocha Soares; Fabrício Mendes Ferreira; Christiane França Coimbra; André Luiz Lopez Sampaio; Carlos Augusto Costa Pires De Oliveira Journal: Case Rep Neurol Med Date: 2012-07-30