Lian-Ping Sun1, Hui-Ming Jin, Bo Yang, Xiang-Ru Wu. 1. Department of Pediatric Neurosurgery, Xin Hua Hospital Affiliated to Shanghai Jiaotong University, Shanghai, 200092, China. slp1128@126.com
Abstract
BACKGROUND: Juvenile xanthogranuloma (JXG) is a disorder of histiocyte proliferation. Most cases present with a solitary cutaneous lesion. JXG with systemic involvement is rare with significant morbidity. Intracranial solitary JXG may be misdiagnosed before operation. METHODS: A 5-month-old boy showed an elevated anterior fontanel but no other abnormalities on admission. Brain MRI showed a large mass in the right parietal region. RESULTS: The tumor was removed with the encroached meninges. A JXG in the right parietal region was diagnosed pathologically. CONCLUSION: Total excision of the tumor may be curative with a prerequisite of ensuring normal vital signs and nervous function.
BACKGROUND:Juvenile xanthogranuloma (JXG) is a disorder of histiocyte proliferation. Most cases present with a solitary cutaneous lesion. JXG with systemic involvement is rare with significant morbidity. Intracranial solitary JXG may be misdiagnosed before operation. METHODS: A 5-month-old boy showed an elevated anterior fontanel but no other abnormalities on admission. Brain MRI showed a large mass in the right parietal region. RESULTS: The tumor was removed with the encroached meninges. A JXG in the right parietal region was diagnosed pathologically. CONCLUSION: Total excision of the tumor may be curative with a prerequisite of ensuring normal vital signs and nervous function.
Authors: Liliana Pagura; Inmaculada de Prada; Miguel Angel López-Pino; Juan Gabriel Huertas; Francisco Villarejo Journal: Childs Nerv Syst Date: 2014-10-04 Impact factor: 1.475
Authors: Sherise D Ferguson; Steven G Waguespack; Lauren A Langford; Joann L Ater; Ian E McCutcheon Journal: Childs Nerv Syst Date: 2014-12-12 Impact factor: 1.475