Literature DB >> 19162063

Collagen VI myopathies: from the animal model to the clinical trial.

Nadir M Maraldi1, Patrizia Sabatelli, Marta Columbaro, Alessandra Zamparelli, Francesco A Manzoli, Paolo Bernardi, Paolo Bonaldo, Luciano Merlini.   

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Year:  2009        PMID: 19162063     DOI: 10.1016/j.advenzreg.2008.12.009

Source DB:  PubMed          Journal:  Adv Enzyme Regul        ISSN: 0065-2571


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  12 in total

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Review 3.  Extracellular matrix molecules: potential targets in pharmacotherapy.

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4.  Absence of type VI collagen paradoxically improves cardiac function, structure, and remodeling after myocardial infarction.

Authors:  Daniel J Luther; Charles K Thodeti; Patricia E Shamhart; Ravi K Adapala; Cheryl Hodnichak; Dorothee Weihrauch; Paolo Bonaldo; William M Chilian; J Gary Meszaros
Journal:  Circ Res       Date:  2012-02-16       Impact factor: 17.367

5.  Mesenchymal condensation-dependent accumulation of collagen VI stabilizes organ-specific cell fates during embryonic tooth formation.

Authors:  Tadanori Mammoto; Akiko Mammoto; Amanda Jiang; Elisabeth Jiang; Basma Hashmi; Donald E Ingber
Journal:  Dev Dyn       Date:  2015-04-24       Impact factor: 3.780

6.  Changes in muscle cell metabolism and mechanotransduction are associated with myopathic phenotype in a mouse model of collagen VI deficiency.

Authors:  Sara De Palma; Roberta Leone; Paolo Grumati; Michele Vasso; Roman Polishchuk; Daniele Capitanio; Paola Braghetta; Paolo Bernardi; Paolo Bonaldo; Cecilia Gelfi
Journal:  PLoS One       Date:  2013-02-20       Impact factor: 3.240

7.  Antamanide, a derivative of Amanita phalloides, is a novel inhibitor of the mitochondrial permeability transition pore.

Authors:  Luca Azzolin; Nicola Antolini; Andrea Calderan; Paolo Ruzza; Marco Sciacovelli; Oriano Marin; Stefano Mammi; Paolo Bernardi; Andrea Rasola
Journal:  PLoS One       Date:  2011-01-28       Impact factor: 3.240

8.  ColVI myopathies: where do we stand, where do we go?

Authors:  Valérie Allamand; Laura Briñas; Pascale Richard; Tanya Stojkovic; Susana Quijano-Roy; Gisèle Bonne
Journal:  Skelet Muscle       Date:  2011-09-23       Impact factor: 4.912

9.  Deep RNA profiling identified CLOCK and molecular clock genes as pathophysiological signatures in collagen VI myopathy.

Authors:  Chiara Scotton; Matteo Bovolenta; Elena Schwartz; Maria Sofia Falzarano; Elena Martoni; Chiara Passarelli; Annarita Armaroli; Hana Osman; Carmelo Rodolico; Sonia Messina; Elena Pegoraro; Adele D'Amico; Enrico Bertini; Francesca Gualandi; Marcella Neri; Rita Selvatici; Patrizia Boffi; Maria Antonietta Maioli; Hanns Lochmüller; Volker Straub; Katherine Bushby; Tiziana Castrignanò; Graziano Pesole; Patrizia Sabatelli; Luciano Merlini; Paola Braghetta; Paolo Bonaldo; Paolo Bernardi; Reghan Foley; Sebahattin Cirak; Irina Zaharieva; Francesco Muntoni; Daniele Capitanio; Cecilia Gelfi; Ekaterina Kotelnikova; Anton Yuryev; Michael Lebowitz; Xiping Zhang; Brian A Hodge; Karyn A Esser; Alessandra Ferlini
Journal:  J Cell Sci       Date:  2016-03-04       Impact factor: 5.285

10.  Discovery, Synthesis, and Optimization of Diarylisoxazole-3-carboxamides as Potent Inhibitors of the Mitochondrial Permeability Transition Pore.

Authors:  Sudeshna Roy; Justina Šileikytė; Marco Schiavone; Benjamin Neuenswander; Francesco Argenton; Jeffrey Aubé; Michael P Hedrick; Thomas D Y Chung; Michael A Forte; Paolo Bernardi; Frank J Schoenen
Journal:  ChemMedChem       Date:  2015-08-18       Impact factor: 3.466

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