Literature DB >> 19129697

Audiometric characteristics of USH2a patients.

Joop M Leijendeckers1, Ronald J E Pennings, Ad F M Snik, Arjan J Bosman, Cor W R J Cremers.   

Abstract

Temporal processing, frequency discrimination and frequency resolution, three basic mechanisms involved in speech perception, were studied in 11 USH2a patients from 10 Dutch families. Measurements included loudness scaling, gap detection, determination of auditory filter shapes and difference limen for frequency. The results were compared to values obtained from listeners with normal hearing, DFNA8/12 patients, DFNA13 patients and unselected patients with presbyacusis. Overall, the results for USH2a were most similar to those obtained in patients with sensorineural hearing loss caused by hair cell defects. To our knowledge, this is the first study that presents results on audiometric measurements combined with psychophysical measurements in a group of USH2a patients.

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Year:  2009        PMID： 19129697     DOI： 10.1159/000189265

Source DB:  PubMed          Journal:  Audiol Neurootol        ISSN： 1420-3030            Impact factor:   1.854


  7 in total

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