| Literature DB >> 19089668 |
R Díaz Nieto1, A Arjona Sánchez, M Gómez Alvarez, D Martínez Cecilia, J M Sánchez Hidalgo, R Ciria Bru, M C Pérez Manrique, J Sánchez Rodríguez, S Rufián Peña.
Abstract
INTRODUCTION: Carney's triad is a rare pathogenic entity which consists of the association in young women of multiple condromatosis in the lung, gastric leiomyosarcoma, and extradrenal paraganglioma; although the presence of three at the same time is not required for its diagnosis. CASE REPORT: We present the case of a 27-year-old woman who was diagnosed of pulmonary multiple hamartomatosis and gastric stromal tumor. DISCUSSION: A review of the literature shows the most important prognosis factors and therapeutic options. Surgery for gastrointestinal stromal tumors and extradrenal paraganglioma seems to be the best treatment up to date.Entities:
Mesh：
Year: 2007 PMID： 19089668 DOI： 10.1007/s12029-008-9026-y
Source DB: PubMed Journal: J Gastrointest Cancer