Literature DB >> 1905194

Surgical treatment of colonic ganglioneuromatosis in neurofibromatosis.

J D Urschel1, R C Berendt, J E Anselmo.   

Abstract

Gastrointestinal involvement in neurofibromatosis occurs in three forms: neurofibromatous tumours, visceral vasculopathy and ganglioneuromatosis. A case of colonic ganglioneuromatosis is reported and six similar cases from the literature are reviewed. The clinical and pathological features of this condition are summarized and guidelines for surgical therapy formulated. Subtotal colectomy is recommended for pseudo-obstructive symptoms refractory to medical management.

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Year:  1991        PMID: 1905194

Source DB:  PubMed          Journal:  Can J Surg        ISSN: 0008-428X            Impact factor:   2.089


  6 in total

1.  Intra-abdominal plexiform neurofibromatosis including periportal, mesentery, and gastrointestinal tract involvement in neurofibromatosis type 1: case report and review of the literature.

Authors:  Takashi Fujisawa; Masafumi Takata; Sachiko Ouchi; Shigemitsu Ueyama; Takahiro Nakajima; Masaaki Mitsutsuji; Takashi Kawamura; Masanori Toyoda; Akiji Okamura
Journal:  Clin J Gastroenterol       Date:  2011-07-24

2.  Intestinal ganglioneuromatosis: an unusual aetiology for occult gastrointestinal bleeding.

Authors:  Alexandra Fernandes; Ana Margarida Ferreira; Paula Serra; Luís Carvalho
Journal:  BMJ Case Rep       Date:  2015-09-30

3.  Evaluation of gastrointestinal hemorrhage in patients with neurofibromatosis.

Authors:  I A Mustafa; W P Reed; N P Coe
Journal:  Surg Endosc       Date:  1994-07       Impact factor: 4.584

4.  Isolated intestinal neurofibromatous proliferations in the absence of associated systemic syndromes.

Authors:  J-Elliot Carter; Javier-A Laurini
Journal:  World J Gastroenterol       Date:  2008-11-14       Impact factor: 5.742

5.  Diffuse Intestinal Ganglioneuromatosis Showing Multiple Large Bowel Ulcers in a Patient with Neurofibromatosis Type 1.

Authors:  Masaya Iwamuro; Rika Omote; Takehiro Tanaka; Naruhiko Sunada; Takahiro Nada; Yoshitaka Kondo; Soichiro Nose; Mitsuhiko Kawaguchi; Fumio Otsuka; Hiroyuki Okada
Journal:  Intern Med       Date:  2017-10-11       Impact factor: 1.271

6.  Neurofibroma discharged from the anus with stool: A case report and review of literature.

Authors:  Yu Miao; Jian-Jiang Wang; Zhi-Ming Chen; Jia-Lian Zhu; Mu-Bin Wang; Sheng-Qiang Cai
Journal:  World J Clin Cases       Date:  2018-10-06       Impact factor: 1.337

  6 in total

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