Secondary vasoproliferative retinal tumor associated with Usher syndrome type 1.

Vasoproliferative retinal tumors are benign tumors of unknown origin that generally affect healthy persons between their fourth and sixth decades and may lead to severe vision loss as a result of intraretinal hemorrhages and exudates. They must be differentiated from retinal capillary hemangiomas of von Hippel-Lindau disease, retinal astrocytoma, Coats disease, peripheral exudative hemorrhagic chorioretinopathy, choroidal melanomas, and retinal/choroidal metastasis. We describe a case of unilateral vasoproliferative retinal tumor associated with retinitis pigmentosa in a patient with Usher syndrome type 1.