| Literature DB >> 19003752 |
P Katsinelos1, T Vasiliadis, K Soufleris, G Chatzimavroudis, C Zavos, G Paroutoglou, T Katsinelos, B Papaziogas, J Kountouras.
Abstract
Congenital afibrinogenemia is a rare genetic disorder characterized by the complete absence of functional fibrinogen. We report a 22-year-old female who developed nephrogenic arterial hypertension and intestinal ischemia due to congenital afibrinogenemia-associated angiopathy of large abdominal arteries. We describe, for the first time, the capsule findings and discuss the pathophysiology of this unusual condition.Entities:
Mesh：
Year: 2008 PMID： 19003752 DOI： 10.1024/0301-1526.37.4.383
Source DB: PubMed Journal: Vasa ISSN： 0301-1526 Impact factor: 1.961