Literature DB >> 1898534

Branched-chain amino acid-free parenteral nutrition in the treatment of acute metabolic decompensation in patients with maple syrup urine disease.

G T Berry1, R Heidenreich, P Kaplan, F Levine, A Mazur, M J Palmieri, M Yudkoff, S Segal.   

Abstract

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Year:  1991        PMID： 1898534     DOI： 10.1056/NEJM199101173240307

Source DB:  PubMed          Journal:  N Engl J Med        ISSN： 0028-4793            Impact factor:   91.245


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  8 in total

1.  Postoperative metabolic decompensation in maple syrup urine disease is completely prevented by insulin.

Authors:  B Biggemann; R Zass; U Wendel
Journal:  J Inherit Metab Dis       Date:  1993       Impact factor: 4.982

2.  Parenteral administration of amino acids in disorders of branched-chain amino acid metabolism.

Authors:  W Sperl; D Skladal; W Endres; G Speer; K Groke
Journal:  J Inherit Metab Dis       Date:  1994       Impact factor: 4.982

3.  Seroprevalence of astrovirus types 1 and 6 in London, determined using recombinant virus antigen.

Authors:  S Kriston; M M Willcocks; M J Carter; W D Cubitt
Journal:  Epidemiol Infect       Date:  1996-08       Impact factor: 2.451

4.  Treatment of acute decompensation of maple syrup urine disease in adult patients with a new parenteral amino-acid mixture.

Authors:  A Servais; J B Arnoux; C Lamy; A Hummel; N Vittoz; I Katerinis; V Bazzaoui; S Dubois; C Broissand; M C Husson; M P Berleur; D Rabier; C Ottolenghi; V Valayannopoulos; P de Lonlay
Journal:  J Inherit Metab Dis       Date:  2012-12-19       Impact factor: 4.982

5.  Biochemical correlates of neuropsychiatric illness in maple syrup urine disease.

Authors:  Emilie R Muelly; Gregory J Moore; Scott C Bunce; Julie Mack; Don C Bigler; D Holmes Morton; Kevin A Strauss
Journal:  J Clin Invest       Date:  2013-03-08       Impact factor: 14.808

6.  Intellectual performance of children with maple syrup urine disease.

Authors:  C Hilliges; D Awiszus; U Wendel
Journal:  Eur J Pediatr       Date:  1993-02       Impact factor: 3.183

Review 7.  Emergency management of inherited metabolic diseases.

Authors:  V Prietsch; M Lindner; J Zschocke; W L Nyhan; G F Hoffmann
Journal:  J Inherit Metab Dis       Date:  2002-11       Impact factor: 4.982

8.  Intravenous branched-chain amino-acid-free solution for the treatment of metabolic decompensation episodes in Spanish pediatric patients with maple syrup urine disease.

Authors:  Paula Sánchez-Pintos; Silvia Meavilla; María Goretti López-Ramos; Ángeles García-Cazorla; Maria L Couce
Journal:  Front Pediatr       Date:  2022-08-15       Impact factor: 3.569
  8 in total

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