Vijay Parihar1, Yad Ram Yadav, Dhananjaya Sharma. 1. Assistant Professor Neurosurgery, Neurosurgery Unit, Department of General Surgery, NSCB Govt, Medical College & Hospital, Jabalpur, MP, 482002, India. drvijayparihar@gmail.com.
Abstract
INTRODUCTION: Gorham's disease is a rare bone disease, is characterized by the proliferation of thin-walled vascular channels associated with regional osteolysis. There have been fewer than 150 cases reported in the literature. Shoulder and pelvic region is common site. Skull is the least common site of involvement. CASE PRESENTATION: We describe a case of a 35-year-old female of Indian origin presented with this rare condition involving her left parietal bone. She was treated successfully with excision of diseased bone and cranioplasty. CONCLUSION: This is the first reported case in India. We provide a review of the clinical, radiological and pathological diagnosis of this rare condition and describe treatment options.
INTRODUCTION:Gorham's disease is a rare bone disease, is characterized by the proliferation of thin-walled vascular channels associated with regional osteolysis. There have been fewer than 150 cases reported in the literature. Shoulder and pelvic region is common site. Skull is the least common site of involvement. CASE PRESENTATION: We describe a case of a 35-year-old female of Indian origin presented with this rare condition involving her left parietal bone. She was treated successfully with excision of diseased bone and cranioplasty. CONCLUSION: This is the first reported case in India. We provide a review of the clinical, radiological and pathological diagnosis of this rare condition and describe treatment options.
Authors: So Young Yoo; Sung Hwan Hong; Hye Won Chung; Jung-Ah Choi; Chong Jai Kim; Heung Sik Kang Journal: Skeletal Radiol Date: 2002-03-15 Impact factor: 2.199
Authors: Catherine E de Keyser; Michael S Saltzherr; Eelke M Bos; M Carola Zillikens Journal: Front Endocrinol (Lausanne) Date: 2020-02-05 Impact factor: 5.555