[Renal agenesis, bicornuate uterus and cyst of the Gartner's duct].

A cyst of Gartner's duct with a bicornuate, unicervical uterus and ipsilateral renal agenesis were seen in a 13-month-old girl. Left renal agenesis had been suggested by antenatal ultrasound findings. After birth, there were no symptoms but ultrasonography demonstrated a multicystic mass in the pelvis. Diagnosis was confirmed by histological study of the mass which had been completely removed during surgery. This infrequent genitourinary malformation is due to a developmental abnormality of the wolffian duct early in fetal life. This case is the eighth report in the literature. Course can be complicated by abscess formation and malignant transformation but most patients remain symptom-free. Treatment is discussed.