BACKGROUND: Primitive neuroectodermal tumours (PNETs) constitute a family of neoplasms of presumed neuroectodermal origin that predominantly present as bone or soft-tissue masses in adolescents and young adults. PNET arising in the kidney is rare. OBJECTIVE: To describe the radiological features in three patients with primary renal PNET. MATERIALS AND METHODS: The radiological features of primary renal PNET in three adolescent patients (age 10, 14 and 16 years) are described. RESULTS: Tumour thrombus extending into the renal vein and inferior vena cava was noted in all three patients. In addition, further tumour extension into the atrium was seen in two patients with extension into a pulmonary artery in one patient. Neural foraminal and intraspinal extension close to the origin of the tumour was identified in two patients. Liver, bone and lung metastases were identified. CONCLUSION: While rare, one should consider the diagnosis of PNET when encountering a renal mass with aggressive features such as inferior vena cava tumour thrombus, direct intraspinal invasion and distant metastasis.
BACKGROUND:Primitive neuroectodermal tumours (PNETs) constitute a family of neoplasms of presumed neuroectodermal origin that predominantly present as bone or soft-tissue masses in adolescents and young adults. PNET arising in the kidney is rare. OBJECTIVE: To describe the radiological features in three patients with primary renal PNET. MATERIALS AND METHODS: The radiological features of primary renal PNET in three adolescent patients (age 10, 14 and 16 years) are described. RESULTS:Tumour thrombus extending into the renal vein and inferior vena cava was noted in all three patients. In addition, further tumour extension into the atrium was seen in two patients with extension into a pulmonary artery in one patient. Neural foraminal and intraspinal extension close to the origin of the tumour was identified in two patients. Liver, bone and lung metastases were identified. CONCLUSION: While rare, one should consider the diagnosis of PNET when encountering a renal mass with aggressive features such as inferior vena cava tumour thrombus, direct intraspinal invasion and distant metastasis.
Authors: Elise Perer; Allan M Shanberg; Garrett Matsunaga; Jerry Z Finklestein Journal: J Laparoendosc Adv Surg Tech A Date: 2006-02 Impact factor: 1.878
Authors: Rafael E Jimenez; Andrew L Folpe; Rosanna L Lapham; Jae Y Ro; Patricia A O'Shea; Sharon W Weiss; Mahul B Amin Journal: Am J Surg Pathol Date: 2002-03 Impact factor: 6.394
Authors: Justine N van der Beek; Tom A Watson; Rutger A J Nievelstein; Hervé J Brisse; Carlo Morosi; Henrique M Lederman; Ana Coma; Maria M Gavra; Kristina Vult von Steyern; Karoly Lakatos; Luc Breysem; Edit Varga; Hubert Ducou Le Pointe; Maarten H Lequin; Jürgen F Schäfer; Hans-Joachim Mentzel; Andreas M Hötker; Giuseppina Calareso; Sophie Swinson; Martin Kyncl; Claudio Granata; Michael Aertsen; Pier Luigi Di Paolo; Ronald R de Krijger; Norbert Graf; Øystein E Olsen; Jens-Peter Schenk; Marry M van den Heuvel-Eibrink; Annemieke S Littooij Journal: J Magn Reson Imaging Date: 2021-08-06 Impact factor: 5.119