Extraskeletal osteosarcoma of the orbit.

Patient. We report a 22-year-old male presenting with extraskeletal osteosarcoma of the orbit.Discussion. Extra skeletal osteosarcomas are uncommon tumours, usually arising from the lower extremities or girdle. These are aggressive tumours with high metastatic potential and poor outcome. Optimal treatment is undefined, and the role of radical surgery, radiotherapy and aggressive chemotherapy is currently being evaluated. The orbit is a rare site for extraskeletal osteosarcoma, with the only previous case reported in an 11-year-old male, who was irradiated in infancy for a retinoblastoma.