Literature DB >> 18439097

Peutz-jeghers syndrome and colon cancer in a 10-year-old girl: implications for when and how to start screening?

Surachai Saranrittichai1.   

Abstract

The Peutz-Jeghers syndrome (PJS) is characterized by hamartomatous polyposis of the gastro-intestinal (GI) tract, with mucocutaneous pigmentation. We have experienced a case of a 10-year-old girl who presented with PJS, intussusception, colonic perforation and colonic adenocarcinoma. Finally, this case developed airway obstruction from the mediastinal mass. In order to prevent cancer and short bowel syndrome, aggressive screening is recommended.

Entities:  

Mesh：

Year:  2008        PMID： 18439097

Source DB:  PubMed          Journal:  Asian Pac J Cancer Prev        ISSN： 1513-7368


  4 in total

1.  Peutz-Jeghers syndrome: need for early screening.

Authors:  Kashish Khanna; Vikram Khanna; Veereshwar Bhatnagar
Journal:  BMJ Case Rep       Date:  2018-12-13

2.  Unusually early presentation of small-bowel adenocarcinoma in a patient with Peutz-Jeghers syndrome.

Authors:  Michael F Wangler; Rishikesh Chavan; M John Hicks; Jed G Nuchtern; Madhuri Hegde; Sharon E Plon; Patrick A Thompson
Journal:  J Pediatr Hematol Oncol       Date:  2013-05       Impact factor: 1.289

Review 3.  Peutz-Jeghers syndrome: diagnostic and therapeutic approach.

Authors:  Marcela Kopacova; Ilja Tacheci; Stanislav Rejchrt; Jan Bures
Journal:  World J Gastroenterol       Date:  2009-11-21       Impact factor: 5.742

4.  Multifocal Jejuno-ileal carcinoma in a 7-year-old boy with Peutz-Jeghers syndrome: A rare occurence.

Authors:  Richa Ranjan; Devajit Nath; Santosh Dey; Sudheer Arava
Journal:  Indian J Med Paediatr Oncol       Date:  2014-01
  4 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.