Literature DB >> 18427982

The use of CDME in cystinosis research.

Martijn J Wilmer1, Lambertus P van den Heuvel, Elena N Levtchenko.   

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Year:  2008        PMID： 18427982     DOI： 10.1007/s11064-008-9709-6

Source DB:  PubMed          Journal:  Neurochem Res        ISSN： 0364-3190            Impact factor:   3.996


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  13 in total

1.  Elevated oxidized glutathione in cystinotic proximal tubular epithelial cells.

Authors:  Martijn J G Wilmer; Adriana de Graaf-Hess; Henk J Blom; Henry B P M Dijkman; Leo A Monnens; Lambertus P van den Heuvel; Elena N Levtchenko
Journal:  Biochem Biophys Res Commun       Date:  2005-09-23       Impact factor: 3.575

2.  Rupture of rat liver lysosomes mediated by L-amino acid esters.

Authors:  R Goldman; A Kaplan
Journal:  Biochim Biophys Acta       Date:  1973-08-22

3.  Intralysosomal cystine accumulation in mice lacking cystinosin, the protein defective in cystinosis.

Authors:  Stéphanie Cherqui; Caroline Sevin; Ghislaine Hamard; Vasiliki Kalatzis; Mireille Sich; Marie O Pequignot; Karïn Gogat; Marc Abitbol; Michel Broyer; Marie-Claire Gubler; Corinne Antignac
Journal:  Mol Cell Biol       Date:  2002-11       Impact factor: 4.272

4.  Mechanisms for the cytotoxicity of cysteamine.

Authors:  T M Jeitner; D A Lawrence
Journal:  Toxicol Sci       Date:  2001-09       Impact factor: 4.849

5.  Exfoliated human proximal tubular cells: a model of cystinosis and Fanconi syndrome.

Authors:  Guido F Laube; Mushfequr R Haq; William G van't Hoff
Journal:  Pediatr Nephrol       Date:  2004-12-31       Impact factor: 3.714

6.  Lysosomal cystine storage augments apoptosis in cultured human fibroblasts and renal tubular epithelial cells.

Authors:  Margaret Park; Amanda Helip-Wooley; Jess Thoene
Journal:  J Am Soc Nephrol       Date:  2002-12       Impact factor: 10.121

7.  Cystine dimethylester model of cystinosis: still reliable?

Authors:  Martijn J Wilmer; Peter H Willems; Sjoerd Verkaart; Henk-Jan Visch; Adriana de Graaf-Hess; Henk J Blom; Leo A Monnens; Lambertus P van den Heuvel; Elena N Levtchenko
Journal:  Pediatr Res       Date:  2007-08       Impact factor: 3.756

8.  Antioxidant effect of cysteamine in brain cortex of young rats.

Authors:  Adriana Kessler; Micheli Biasibetti; Denizar Alberto da Silva Melo; Moacir Wajner; Carlos Severo Dutra-Filho; Angela Terezinha de Souza Wyse; Clovis Milton Duval Wannmacher
Journal:  Neurochem Res       Date:  2007-10-17       Impact factor: 3.996

9.  Accumulation of amino acids by lysosomes incubated with amino acid methyl esters.

Authors:  J P Reeves
Journal:  J Biol Chem       Date:  1979-09-25       Impact factor: 5.157

10.  Impaired activity of the gamma-glutamyl cycle in nephropathic cystinosis fibroblasts.

Authors:  Liliana Mannucci; Anna Pastore; Cristiano Rizzo; Fiorella Piemonte; Gianfranco Rizzoni; Francesco Emma
Journal:  Pediatr Res       Date:  2006-02       Impact factor: 3.756
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  4 in total

Review 1.  The renal Fanconi syndrome in cystinosis: pathogenic insights and therapeutic perspectives.

Authors:  Stephanie Cherqui; Pierre J Courtoy
Journal:  Nat Rev Nephrol       Date:  2016-12-19       Impact factor: 28.314

2.  Mitochondrial autophagy promotes cellular injury in nephropathic cystinosis.

Authors:  Poonam Sansanwal; Benedict Yen; William A Gahl; Yewei Ma; Lihua Ying; Lee-Jun C Wong; Minnie M Sarwal
Journal:  J Am Soc Nephrol       Date:  2009-12-03       Impact factor: 10.121

Review 3.  Proteinuria and events beyond the slit.

Authors:  Rikke Nielsen; Erik Ilsø Christensen
Journal:  Pediatr Nephrol       Date:  2010-01-05       Impact factor: 3.714

Review 4.  Nephropathic Cystinosis: Pathogenic Roles of Inflammation and Potential for New Therapies.

Authors:  Mohamed A Elmonem; Koenraad R P Veys; Giusi Prencipe
Journal:  Cells       Date:  2022-01-06       Impact factor: 6.600
  4 in total

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