Literature DB >> 1836350

Ichthyosis bullosa of Siemens responds well to low-dosage oral retinoids.

P M Steijlen1, R J van Dooren-Greebe, R Happle, P C Van de Kerkhof.   

Abstract

Two patients with ichthyosis bullosa of Siemens (IBS) and one patient with bullous ichthyosiform erythroderma of Brocq (BIE) were treated with etretinate. Two additional patients with IBS received acitretin. All the patients had a marked improvement when on retinoids and the maintenance dose required was for IBS 10-25 mg per day. The patient with BIE was on a maintenance dose of 40-60 mg per day.

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Year:  1991        PMID: 1836350     DOI: 10.1111/j.1365-2133.1991.tb14776.x

Source DB:  PubMed          Journal:  Br J Dermatol        ISSN: 0007-0963            Impact factor:   9.302


  3 in total

1.  Regulation of keratin expression by retinoids.

Authors:  Hans Törmä
Journal:  Dermatoendocrinol       Date:  2011-07-01

Review 2.  Epidermolytic hyperkeratosis: clinical update.

Authors:  Denice Peter Rout; Anushka Nair; Anand Gupta; Piyush Kumar
Journal:  Clin Cosmet Investig Dermatol       Date:  2019-05-08

Review 3.  Ichthyosis: A Road Model for Skin Research.

Authors:  Anders Vahlquist; Hans Törmä
Journal:  Acta Derm Venereol       Date:  2020-03-25       Impact factor: 3.875

  3 in total

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