Literature DB >> 18351445

Primary immunodeficiency disorders: survey of pediatricians in Kuwait.

Waleed Al-Herz1, Mohammad E Zainal, Mohammad Salama, Wafa Al-Ateeqi, Khalid Husain, Majeda Abdul-Rasoul, Bander Al-Mutairi, Mona Badawi, Najwa Aker, Subodh Kumar, Haitham Al-Khayat.   

Abstract

INTRODUCTION: Early diagnosis of primary immunodeficiency disorders (PID) is critical so life saving interventions can be implemented to avoid significant morbidity and mortality. Unfortunately, they are frequently misdiagnosed, which results into significant delay in diagnosis. This study aimed to determine the knowledge and practice of pediatricians in Kuwait about PID.
MATERIALS AND METHODS: A 66-item self-administered questionnaire was designed and distributed to the pediatricians working at all six governmental hospitals to measure their knowledge and practice about PID. A total of 244 pediatricians (78.4%; 143 males and 101 females) participated in the study. The mean age of participants was 40 years, and the mean number of years working in pediatrics was 13 years. The mean overall score was 59.6%, whereas the mean score in clinical presentation section was 63%, in associated diseases and syndromes section 58%, and in laboratory investigations section 51%. Only 26% of the participants answered correctly at least 2/3 of the questions (67% of the questions).
CONCLUSION: This survey demonstrates that there is universal deficiency in both the knowledge and practice of pediatricians in the field of PID. Implementation of strategies to improve the awareness of pediatricians about PID is critical so early therapeutic interventions can be done to improve the health and prevent morbidity and mortality.

Entities:  

Mesh:

Year:  2008        PMID: 18351445     DOI: 10.1007/s10875-008-9191-6

Source DB:  PubMed          Journal:  J Clin Immunol        ISSN: 0271-9142            Impact factor:   8.317


  19 in total

1.  Common variable immunodeficiency: clinical and immunological features of 248 patients.

Authors:  C Cunningham-Rundles; C Bodian
Journal:  Clin Immunol       Date:  1999-07       Impact factor: 3.969

Review 2.  A historical review of bone marrow transplantation for immunodeficiencies.

Authors:  Rebecca H Buckley
Journal:  J Allergy Clin Immunol       Date:  2004-04       Impact factor: 10.793

3.  Measuring treatment satisfaction in patients with primary immunodeficiency diseases receiving lifelong immunoglobulin replacement therapy.

Authors:  U Nicolay; S Haag; F Eichmann; S Herget; D Spruck; A Gardulf
Journal:  Qual Life Res       Date:  2005-09       Impact factor: 4.147

4.  Population prevalence of diagnosed primary immunodeficiency diseases in the United States.

Authors:  J M Boyle; R H Buckley
Journal:  J Clin Immunol       Date:  2007-06-19       Impact factor: 8.317

Review 5.  Primary immunodeficiency disorders in children: prompt diagnosis can lead to lifesaving treatment.

Authors:  Catherine Champi
Journal:  J Pediatr Health Care       Date:  2002 Jan-Feb       Impact factor: 1.812

6.  Hematopoietic stem cell transplantation for severe combined immunodeficiency in the neonatal period leads to superior thymic output and improved survival.

Authors:  Laurie A Myers; Dhavalkumar D Patel; Jennifer M Puck; Rebecca H Buckley
Journal:  Blood       Date:  2002-02-01       Impact factor: 22.113

7.  Health-related quality of life of children with primary immunodeficiency disease: a comparison study.

Authors:  Kathy Zebracki; Tonya M Palermo; Robert Hostoffer; Kimberly Duff; Dennis Drotar
Journal:  Ann Allergy Asthma Immunol       Date:  2004-12       Impact factor: 6.347

8.  Frequency and clinical manifestations of patients with primary immunodeficiency disorders in Iran: update from the Iranian Primary Immunodeficiency Registry.

Authors:  Nima Rezaei; Asghar Aghamohammadi; Mostafa Moin; Zahra Pourpak; Masoud Movahedi; Mohammad Gharagozlou; Lida Atarod; Bahram Mirsaeid Ghazi; Anna Isaeian; Maryam Mahmoudi; Kamran Abolmaali; Davoud Mansouri; Saba Arshi; Naser Javaher Tarash; Roya Sherkat; Hedayat Akbari; Reza Amin; Abdolvahab Alborzi; Sara Kashef; Reza Farid; Iraj Mohammadzadeh; Mehrnaz Sadeghi Shabestari; Mohammad Nabavi; Abolhassan Farhoudi
Journal:  J Clin Immunol       Date:  2006-10-06       Impact factor: 8.542

9.  Coping, quality of life, and hope in adults with primary antibody deficiencies.

Authors:  Hanne Marie Høybråten Sigstad; Asbjørg Stray-Pedersen; Stig S Frøland
Journal:  Health Qual Life Outcomes       Date:  2005-05-04       Impact factor: 3.186

10.  Primary immunodeficiency disorders in Kuwait: first report from Kuwait National Primary Immunodeficiency Registry (2004--2006).

Authors:  Waleed Al-Herz
Journal:  J Clin Immunol       Date:  2007-11-16       Impact factor: 8.317

View more
  8 in total

1.  Primary immunodeficiency disorders in Iran: update and new insights from the third report of the national registry.

Authors:  Asghar Aghamohammadi; Payam Mohammadinejad; Hassan Abolhassani; Babak Mirminachi; Masoud Movahedi; Mohammad Gharagozlou; Nima Parvaneh; Vaheid Zeiaee; Bahram Mirsaeed-Ghazi; Zahra Chavoushzadeh; Alireza Mahdaviani; Mahboubeh Mansouri; Sedigheh Yousefzadegan; Bahareh Sharifi; Fariborz Zandieh; Ehsan Hedayat; Ali Nadjafi; Roya Sherkat; Behzad Shakerian; Mahnaz Sadeghi-Shabestari; Reza Farid Hosseini; Farahzad Jabbari-Azad; Hamid Ahanchian; Fatemeh Behmanesh; Mohammadreza Zandkarimi; Afshin Shirkani; Taher Cheraghi; Abbas Fayezi; Iraj Mohammadzadeh; Reza Amin; Soheila Aleyasin; Mojgan Moghtaderi; Javad Ghaffari; Saba Arshi; Naser Javahertrash; Mohammad Nabavi; Mohammad Hassan Bemanian; Alireza Shafiei; Najmedin Kalantari; Akefeh Ahmadiafshar; Hossein Ali Khazaei; Lida Atarod; Nima Rezaei
Journal:  J Clin Immunol       Date:  2014-05       Impact factor: 8.317

2.  Primary immunodeficiency diseases in children: 15 year experience in a tertiary care medical center in Qatar.

Authors:  Mohammad S Ehlayel; Abdulbari Bener; Mohammad Abu Laban
Journal:  J Clin Immunol       Date:  2012-10-03       Impact factor: 8.317

3.  Primary Immunodeficiency Diseases in Oman: 10-Year Experience in a Tertiary Care Hospital.

Authors:  Salem Al-Tamemi; Shafiq Ur Rehman Naseem; Nabila Al-Siyabi; Ibtisam El-Nour; Abdulhakim Al-Rawas; David Dennison
Journal:  J Clin Immunol       Date:  2016-10-03       Impact factor: 8.317

4.  Medical awareness concerning primary immunodeficiency diseases in the city of São Paulo, Brazil.

Authors:  Ellen de Oliveira Dantas; Carolina Sanchez Aranda; Fernanda Aimée Nobre; Kristine Fahl; Juliana Themudo Lessa Mazzucchelli; Erika Felix; Dora Lisa Friedlander-Del Nero; Victor Nudelman; Flavio Sano; Antonio Condino-Neto; Elaine Damasceno; Beatriz Tavares Costa-Carvalho
Journal:  Einstein (Sao Paulo)       Date:  2013-12

5.  Comprehensive Genetic Results for Primary Immunodeficiency Disorders in a Highly Consanguineous Population.

Authors:  Waleed Al-Herz; Janet Chou; Ottavia Maria Delmonte; Michel J Massaad; Wayne Bainter; Riccardo Castagnoli; Christoph Klein; Yenan T Bryceson; Raif S Geha; Luigi D Notarangelo
Journal:  Front Immunol       Date:  2019-01-15       Impact factor: 7.561

6.  Attentiveness of pediatricians to primary immunodeficiency disorders.

Authors:  Suleiman Al-Hammadi; Eiman Al-Reyami; Sareea Al-Remeithi; Khawla Al-Zaabi; Rola Al-Zir; Heba Al-Sagban; Taoufik Zoubaidi; Abdul-Kader Souid
Journal:  BMC Res Notes       Date:  2012-07-31

7.  The value of family history in diagnosing primary immunodeficiency disorders.

Authors:  Mohamed A Hendaus; Ahmad Alhammadi; Mehdi M Adeli; Fawzia Al-Yafei
Journal:  Case Rep Pediatr       Date:  2014-08-05

8.  National Survey about awareness of Primary Immunodeficiency Disorders among Primary Care Physicians in Saudi Arabia: Protocol and Challenges.

Authors:  Areej AlFattani; Fatimah Rabhan; Lujain AlAssaf; Amal Alghammas; Edward De Vol
Journal:  J Prim Care Community Health       Date:  2020 Jan-Dec
  8 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.