Spontaneous perforation of the bile duct.

BACKGROUND: Spontaneous perforation of the bile ducts is a rare condition in adults. It is commonly secondary to gallstones, and the site of the perforation is nearly always extrahepatic. Intrahepatic perforation has only once been described in the literature to date. CASE OUTLINE: We report an unusual presentation of this condition with perforation occurring at an intrahepatic site. The management of perforation and the possible predisposing factors are described. DISCUSSION: Adequate management of this problem requires an awareness of its existence and prompt, appropriate investigation to discover the cause and site of perforation.