Literature DB >> 18245975

A novel mutation as the basis for asymptomatic meesmann dystrophy in a Danish family.

Kim Nielsen1, Torben Orntoft, Jesper Hjortdal, Tommy Rasmussen, Niels Ehlers.   

Abstract

PURPOSE: Meesmann dystrophy is a rare inherited corneal disease. This is the description of a unique family in Denmark.
METHODS: The family members were examined by biomicroscopy. Blood samples were collected. DNA from the leukocyte population was isolated, and the cytokeratin 12 (KRT12) gene was partially sequenced.
RESULTS: This Danish family harbors a 451G-->T mutation. All patients in this family that harbor mutations also show microcysts, but none have any symptoms.
CONCLUSIONS: This is the second family recently diagnosed with Meesmann dystrophy in Denmark. The family represents its own distinct genotype, independent of previously reported ones. All patients with microcysts were asymptomatic.

Entities:  

Mesh:

Substances:

Year:  2008        PMID: 18245975     DOI: 10.1097/ICO.0b013e31815652fd

Source DB:  PubMed          Journal:  Cornea        ISSN: 0277-3740            Impact factor:   2.651


  6 in total

1.  Novel mutations in the keratin-74 (KRT74) gene underlie autosomal dominant woolly hair/hypotrichosis in Pakistani families.

Authors:  Naveed Wasif; Syed Kamran ul-Hassan Naqvi; Sulman Basit; Nadir Ali; Muhammad Ansar; Wasim Ahmad
Journal:  Hum Genet       Date:  2010-12-28       Impact factor: 4.132

2.  Identification of a novel mutation in the cornea specific keratin 12 gene causing Meesmann's corneal dystrophy in a German family.

Authors:  Ina Clausen; Gernot I W Duncker; Claudia Grünauer-Kloevekorn
Journal:  Mol Vis       Date:  2010-05-29       Impact factor: 2.367

Review 3.  The molecular basis of human keratin disorders.

Authors:  Meral Julia Arin
Journal:  Hum Genet       Date:  2009-02-27       Impact factor: 4.132

4.  Genetics of Meesmann corneal dystrophy: a novel mutation in the keratin 3 gene in an asymptomatic family suggests genotype-phenotype correlation.

Authors:  Jacek P Szaflik; Monika Ołdak; Radosław B Maksym; Anna Kamińska; Agnieszka Pollak; Monika Udziela; Rafał Płoski; Jerzy Szaflik
Journal:  Mol Vis       Date:  2008-09-15       Impact factor: 2.367

5.  Identification of presumed pathogenic KRT3 and KRT12 gene mutations associated with Meesmann corneal dystrophy.

Authors:  Judy L Chen; Benjamin R Lin; Katherine M Gee; Jessica A Gee; Duk-Won D Chung; Ricardo F Frausto; Sophie X Deng; Anthony J Aldave
Journal:  Mol Vis       Date:  2015-12-31       Impact factor: 2.367

6.  Identification of a Novel Missense KRT12 Mutation in a Vietnamese Family with Meesmann Corneal Dystrophy.

Authors:  Pham Ngoc Dong; Le Xuan Cung; Tran Khanh Sam; Do Thi Thuy Hang; Doug D Chung; Turad A Alkadi; Arjun Buckshey; Junwei Zhang; Alexa Kassels; Anthony J Aldave
Journal:  Case Rep Ophthalmol       Date:  2020-03-17
  6 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.