Literature DB >> 18176178

A case of congenital peripheral primitive neuroectodermal tumor presenting with multiple metastases.

Cristina Meazza1, Andrea Ferrari, Monica Fumagalli, Paola Collini, Michela Casanova, Lorenza Pugni, Mariarosa Colnaghi, Elena Zaffignani, Marta Podda, Fabio Mosca.   

Abstract

The report describes a case of a newborn with a huge congenital abdominal peripheral primitive neuroectodermal tumor, with peritoneal dissemination and cutaneous involvement, and discusses literature data. Peripheral primitive neuroectodermal tumor is an exceedingly uncommon tumor in this age group and is characterized by very aggressive behavior and poor prognosis.

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Year:  2008        PMID: 18176178     DOI: 10.1097/MPH.0b013e31815cf730

Source DB:  PubMed          Journal:  J Pediatr Hematol Oncol        ISSN: 1077-4114            Impact factor:   1.289


  2 in total

1.  Solitary epidural brain metastasis of a peripheral neuroepithelioma (a primitive neuroectodermal tumor): a case report.

Authors:  Atoosa Adibi; Roozbeh Barikbin; Navid Koleini; Maryam Farghadani; Kourosh Mougouei; Farnaz Farshidfar
Journal:  J Radiol Case Rep       Date:  2008-07-01

2.  Congenital sacrococcygeal PNET and chemotherapy.

Authors:  Colin Patrick Hawkes; David R Betts; John O'Brien; Maureen J O'Sullivan; Michael Capra
Journal:  Indian J Med Paediatr Oncol       Date:  2012-07
  2 in total

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