[Sinusal teratocarcinosarcoma].

We present a case of a very rare naso-sinusal malignant, teratoid neoplasia, recently called "terato-carcinosarcoma". The tumor appeared in right sinuses of a 18 year old male with nasal obstruction, headache and unilateral proptosis. In spite of surgery and radiotherapy, the patient showed, 4 months later, local massive relapse. Treatment was considered to not be possible. We review the literature about this topic, and we only find 26 published cases; the presented case would be the first published one in our country.