Airway considerations in craniofacial patients.

Children with syndromic craniosynostosis have an increased risk of airway obstruction. Addressing this issue early in their clinical course helps ensure a safe result. Because of their abnormal airways and a higher risk of sleep-related breathing disorders, regular evaluation of the airway is recommended. An algorithm for evaluation, including sleep study, and management of such children is proposed. Patients with abnormal sleep studies should undergo endoscopy (nasendoscopy or flexible fiberoptic bronchoscopy) to determine the site of the obstruction and then adenotonsillectomy when appropriate. Continuous positive airway pressure, nasopharyngeal airways, or surgery, including osteotomy or even tracheostomy, may be necessary. Regular evaluation of the airway is critical, because the airway status may improve or worsen with growth of the child. Finally, ongoing communication with the craniofacial team allows planning of various procedures in the individual patient with optimal management of the airway.