Literature DB >> 18043389

A variant of Poland syndrome associated with dextroposition.

Hakan Mutlu1, Onur Sildiroglu, Cinar C Basekim, Esref Kizilkaya.   

Abstract

Poland syndrome is characterized by partial or complete absence of pectoralis muscles, ipsilateral syndactyly, and occasionally other malformations of the anterior chest wall and breast. Other associated anomalies, including dextrocardia, renal malformations, and vertebral anomalies, have been reported in rare cases. The condition is more frequent among males, and usually occurs on the right hemithorax in the unilateral form. The syndrome is believed to be caused by a genetic disorder that reduces the embryonal circulation in the subclavian and vertebral arteries. We report a 20-year-old man with Poland syndrome on the left hemithorax, which is rarely associated with dextroposition.

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Year:  2007        PMID: 18043389     DOI: 10.1097/01.rti.0000184831.84395.05

Source DB:  PubMed          Journal:  J Thorac Imaging        ISSN: 0883-5993            Impact factor:   3.000


  3 in total

1.  Left-sided Poland's syndrome in a girl with rare associations like spina bifida and diaphragmatic hernia.

Authors:  V C Sunitha; Sathya Narayanan; Pradeep Pankajakshan Nair; Manikka Lakshmanan Prakash
Journal:  BMJ Case Rep       Date:  2013-09-20

2.  A case of Poland Syndrome associated with dextroposition.

Authors:  Doriana Lacorte; Maria Marsella; Pietro Guerrini
Journal:  Ital J Pediatr       Date:  2010-02-20       Impact factor: 2.638

Review 3.  Anaesthesia for chest wall reconstruction in a patient with Poland syndrome: CARE-compliant case report and literature review.

Authors:  Lingli Gui; Shiqian Shen; Wei Mei
Journal:  BMC Anesthesiol       Date:  2018-05-24       Impact factor: 2.217

  3 in total

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