Congenital segmental dilatation of the small bowel (CSD).

Congenital segmental dilatation (CSD) is a rare pathology of unknown etiology, usually with early-onset presentation in the neonatal age. We present a case of CSD of the jejunum of a 9-year-old boy with severe malnutrition. Its clinical, radiological and histological features are similar to those described in the literature but the remarkable aspect of this case lies in its late presentation.