[Uterine tumor resembling ovarian sex cord tumor: case report and review of literature].

Uterine tumours with sex cord-like differentiation are rare. They are observed, pre- and post-menopausal women between the fourth and the sixth decade and manifest themselves by haemorrhagic anomalies and usually enlarged uteri, misinterpreted as uterus myomatosus. One distinguishes between two groups on account of the share of sex cord-like elements, i.e. tumours with only focal sex cord-like differentiation with a tendency to relapses and metastatic spread, and tumours with predominant differentiation in the sense of ovarian sex cord tumours with a good prognosis because surgical treatment alone often leads to relapse-free survival. Because of the tumours' rarity, there are no randomized studies as to an optimal therapy. Since there have been reports on endometrial stromal sarcoma with low malignant potential in adjuvant therapy of breast cancer with Tamoxifen, one can assume that this entity will occur more frequently in future.