Literature DB >> 17676373

Chronic granulomatous disease associated with atypical Kawasaki disease.

M A Yamazaki-Nakashimada1, N Ramírez-Vargas, J De Rubens-Figueroa.   

Abstract

Chronic granulomatous disease (CGD) is an infrequent inherited disorder characterized by recurrent infections and abnormal granuloma formation. Patients with CGD have an exuberant inflammatory response and an increased risk of developing autoimmunity. We present the case of a 1-year-old boy with CGD who developed several of the characteristic clinical features of Kawasaki Disease. His illness responded to intravenous immunoglobulin, aspirin, and corticosteroids.

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Year:  2007        PMID: 17676373     DOI: 10.1007/s00246-007-9011-4

Source DB:  PubMed          Journal:  Pediatr Cardiol        ISSN: 0172-0643            Impact factor:   1.838


  20 in total

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5.  Diagnosis, treatment, and long-term management of Kawasaki disease: a statement for health professionals from the Committee on Rheumatic Fever, Endocarditis and Kawasaki Disease, Council on Cardiovascular Disease in the Young, American Heart Association.

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6.  Sarcoidosis in chronic granulomatous disease.

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Review 10.  Systemic lupus erythematosus in a boy with chronic granulomatous disease: case report and review of the literature.

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Journal:  Arthritis Rheum       Date:  1991-01
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  9 in total

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Review 2.  A child with X-linked agammaglobulinemia and Kawasaki disease: an unusual association.

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Journal:  Antioxid Redox Signal       Date:  2014-07-29       Impact factor: 8.401

Review 5.  Kawasaki disease and immunodeficiencies in children: case reports and literature review.

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6.  Presence of a Juvenile Idiopathic Arthritis and Chronic Granulomatous Disease in a Child.

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7.  Kawasaki's disease: An unusual presentation.

Authors:  I Shah
Journal:  J Cardiovasc Dis Res       Date:  2012-07

8.  Genetic, Immunological, and Clinical Features of the First Mexican Cohort of Patients with Chronic Granulomatous Disease.

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Journal:  J Clin Immunol       Date:  2020-02-10       Impact factor: 8.542

9.  Kawasaki disease in a girl with Turner syndrome: a remarkable association.

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  9 in total

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