Literature DB >> 17587626

Thoracic spinal cord compression indicating Wegener's granulomatosis in a patient with a previous presumptive diagnosis of microscopic polyangiitis.

Claude Bachmeyer1, Pascale Cervera, Béatrice Marro, Wafa Ammouri, Eric Bouvard, Pascal Favrole, Frédéric Jacquot, Gilles Grateau.   

Abstract

Neurological signs are observed in 20-50% of cases of Wegener's granulomatosis consisting of peripheral and cranial neuropathy, and central nervous system involvement during the disease and rarely as initial symptom. We report here a case of thoracic spinal cord compression due to dural masses in a patient with a previous presumptive diagnosis of microscopic polyangiitis indicating Wegener's granulomatosis on histological examination. No other site of involvement was found. Slight clinical improvement was observed under immunosuppressive treatment probably because of spinal cord vessels lesions.

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Year:  2007        PMID: 17587626     DOI: 10.1016/j.jbspin.2006.10.008

Source DB:  PubMed          Journal:  Joint Bone Spine        ISSN: 1297-319X            Impact factor:   4.929


  4 in total

Review 1.  Thoracic intradural extramedullary lesions causing progressive myelopathy as an initial manifestation of granulomatosis with polyangiitis: a case report and review of literature.

Authors:  Yuki Taniguchi; Hirotaka Chikuda; Yasushi Oshima; Junichi Ohya; Yoshitaka Matsubayashi; Teppei Morikawa; Harumi Shirai; Oh Sasaki; Mihoko Shibuya; Keishi Fujio; Kazuhiko Yamamoto; Sakae Tanaka
Journal:  J Spinal Cord Med       Date:  2016-04-22       Impact factor: 1.985

2.  Lessons of the month: ANCA-associated vasculitis - granulomatosis with polyangiitis: 'the great mimic'.

Authors:  James Hesford; Andrew Rl Medford; Harsha Gunawardena
Journal:  Clin Med (Lond)       Date:  2021-03       Impact factor: 2.659

3.  Myeloperoxidase-Antineutrophil Cytoplasmic Antibody Positive Hypertrophic Spinal Pachymeningitis at the Cervicothoracic Junction: A Case Report.

Authors:  Ryo Ogaki; Eijiro Okada; Satoshi Suzuki; Satoshi Nori; Osahiko Tsuji; Narihito Nagoshi; Mitsuru Yagi; Kota Watanabe; Masaya Nakamura; Morio Matsumoto
Journal:  Spine Surg Relat Res       Date:  2020-08-20

Review 4.  ANCA-Associated Systemic Vasculitis Presenting With Hypertrophic Spinal Pachymeningitis: A Report of 2 Cases and Review of Literature.

Authors:  Xia Li; Jiuliang Zhao; Qian Wang; Yunyun Fei; Yan Zhao
Journal:  Medicine (Baltimore)       Date:  2015-11       Impact factor: 1.817

  4 in total

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