[Primary ovarian leiomyosarcoma in perimenarche].

Primary ovarian leiomyosarcoma is an extremely rare tumor, which is thought to arise predominantly in postmenopausal women. We report the second case in a perimenarchal adolescent. Diagnosis was grounded on light microscopic and histochemical findings. In our case, the treatment was exclusively surgical. As there was no tumoral residue, and according to the low-grade tumor, no adjuvant treatment was performed.