| Literature DB >> 17383380 |
Eduardo Bernabeu1, Miguel Josa, Benet Nomdedeu, José Ramírez, Antonio García-Valentín, Carlos A Mestres, Jaime Mulet.
Abstract
Wiskott-Aldrich syndrome is a primary immunodeficiency characterized by infections, thrombocytopenia, and eczema. We present a 33-year-old man with this syndrome who underwent a one-stage ascending aorta, aortic arch and descending aortic aneurysm repair under moderate hypothermia and continuous visceral and cerebral perfusion. Histologic examination showed the presence of an aortitis with granulomatous inflammatory response and multinucleated cells.Entities:
Mesh：
Year: 2007 PMID： 17383380 DOI： 10.1016/j.athoracsur.2006.10.005
Source DB: PubMed Journal: Ann Thorac Surg ISSN： 0003-4975 Impact factor: 4.330