Endothelial papillary fibroelastomas arising in and around the aortic sinus, filling the ostium of the right coronary artery.

Endothelial papillary fibroelastomas are rare endocardial and usually valvular lesions, most often found incidentally at autopsy. Occasionally these lesions cause clinical sequelae by embolizing to the heart and brain, or (in the case of valvular ones) by intermittent prolapse into a coronary artery. Papillary fibroelastomas arising in the right coronary ostium, and filling the origin of the right coronary artery are described. Other similar but smaller lesions were found on the surrounding aortic intima. To our knowledge, these are the first such lesions to be described. The case is reviewed in the context of previously published literature on the subject.