Literature DB >> 17333049

[A young fireman candidate with an abnormal chest x-ray].

S Huth1, D Jäger, J Barth.   

Abstract

An 18-year-old, asymptomatic male underwent a routine chest x-ray examination which showed a pathological result. It revealed a characteristic crescent-like shadow in the right lower lung field, resembling a muslim sword (scimitar), responsible for the name of the underlying disease. Scimitar syndrome is a rare congenital malformation with a wide clinical spectrum ranging from asymptomatic to severe disturbances manifesting in childhood. The typical findings are hypoplasia of the right lung with marked mediastinal shift to the right and dextrocardia, reduced right pulmonary artery perfusion with maintained bronchial connection, anomalous arterial supply to the right lower lobe from the aorta and abnormal draining of the enlarged right pulmonary vein into the pulmonary circulation, producing the characteristic radiographic "scimitar sign". The development of right ventricular failure due to long-standing right ventricular overload and recurrent respiratory infections depend on the severity of anatomical abnormalities and functional disorders, sometimes requiring surgical intervention. Nowadays, sophisticated imaging techniques allow precise and rapid diagnosis of these complex abnormalities and their functional implications. The findings for our patient differed from the classic constellation, with a regular emptying of the enlarged right pulmonary vein into the left atrium, leading to a decreased burden on the central haemodynamics. In our very rare case of a scimitar syndrome variant, the functional disorders were negligible.

Entities:  

Mesh:

Year:  2007        PMID: 17333049     DOI: 10.1007/s00108-007-1816-y

Source DB:  PubMed          Journal:  Internist (Berl)        ISSN: 0020-9554            Impact factor:   0.743


  9 in total

1.  The "adult" form of the scimitar syndrome.

Authors:  C Dupuis; L A Charaf; G M Brevière; P Abou; M Rémy-Jardin; G Helmius
Journal:  Am J Cardiol       Date:  1992-08-15       Impact factor: 2.778

2.  Scimitar variant.

Authors:  W Pearl
Journal:  Pediatr Cardiol       Date:  1987       Impact factor: 1.655

3.  Shoe, scimitar or sequestration: a shifting spectrum.

Authors:  A E Boothroyd; H Carty; R Arnold
Journal:  Pediatr Radiol       Date:  1995

4.  Two cases of scimitar variant.

Authors:  S Takeda; T Imachi; K Arimitsu; M Minami; M Hayakawa
Journal:  Chest       Date:  1994-01       Impact factor: 9.410

5.  The scimitar syndrome.

Authors:  M G Foreman; U Rosa
Journal:  South Med J       Date:  1991-04       Impact factor: 0.954

6.  Scimitar syndrome and associated pulmonary sequestration: report of a successfully corrected case.

Authors:  E Horcher; F Helmer
Journal:  Prog Pediatr Surg       Date:  1987

7.  [A case of partial anomalous pulmonary venous return to inferior vena cava and left atrium (Scimitar syndrome)].

Authors:  Y Matsuyama; N Saigusa; M Hioki; S Matsushima; S Tanaka; T Shoji
Journal:  Nihon Kyobu Geka Gakkai Zasshi       Date:  1994-01

8.  Scimitar sign with normal pulmonary venous drainage and systemic arterial supply. Scimitar syndrome or bronchopulmonary sequestration?

Authors:  A Cukier; J Kavakama; L R Teixeira; M Terra-Filho; F S Vargas
Journal:  Chest       Date:  1994-01       Impact factor: 9.410

9.  Inferior vena cava stenosis in scimitar syndrome: a case report.

Authors:  M Jimenez; E Hery; N H van Doesburg; R Guerin; S Spier
Journal:  J Am Soc Echocardiogr       Date:  1988 Mar-Apr       Impact factor: 5.251

  9 in total
  1 in total

1.  Mitochondrial ATP transporter depletion protects mice against liver steatosis and insulin resistance.

Authors:  Joonseok Cho; Yujian Zhang; Shi-Young Park; Anna-Maria Joseph; Chul Han; Hyo-Jin Park; Srilaxmi Kalavalapalli; Sung-Kook Chun; Drake Morgan; Jae-Sung Kim; Shinichi Someya; Clayton E Mathews; Young Jae Lee; Stephanie E Wohlgemuth; Nishanth E Sunny; Hui-Young Lee; Cheol Soo Choi; Takayuki Shiratsuchi; S Paul Oh; Naohiro Terada
Journal:  Nat Commun       Date:  2017-02-16       Impact factor: 14.919

  1 in total

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