| Literature DB >> 17261504 |
Nobuhiro Suzuki1, Naoki Hatakeyama, Masaki Yamamoto, Nobuo Mizue, Yuki Kuroiwa, Minami Yoda, Junko Takahashi, Yoshihiko Tani, Hiroyuki Tsutsumi.
Abstract
Patients with chronic granulomatous disease (CGD) complicated by antimycotics-refractory invasive aspergillosis have an extremely poor prognosis if they cannot undergo allogeneic hematopoietic stem cell transplantation from a suitable related donor while in good clinical condition. We successfully treated a 20-year-old man with very rare McLeod phenotype CGD with reduced-intensity conditioning and unrelated-donor umbilical cord blood transplantation. We postulate that reduced-intensity conditioning-allogeneic hematopoietic stem cell transplantation is a promising therapeutic strategy for patients with CGD even if only unrelated-donor umbilical cord blood is available.Entities:
Mesh:
Year: 2007 PMID: 17261504 DOI: 10.1532/IJH9706129
Source DB: PubMed Journal: Int J Hematol ISSN: 0925-5710 Impact factor: 2.490