Literature DB >> 17235422

[Central core myopathy: a juvenile and adult disease].

H J Gdynia1, A-D Sperfeld, C O Hanemann.   

Abstract

Central core myopathy is a nonprogressive or only slowly progressive congenital muscle disease. In most cases, symptoms begin in childhood, but rare cases with adult onset are described. Regardless of its high variability, the clinical hallmarks are diffuse muscle weakness and the development of multiple bone deformities and contractures. Skeletal muscle biopsy is of high diagnostic significance. Due to a potential association with malignant hyperthermia, early diagnosis is of great importance. A curative treatment is not currently known. Here we discuss aetiology, pathogenesis, clinical features, diagnosis, differential diagnosis, therapeutic strategies, and prognosis of central core myopathy based on a clinical example with an atypical onset of symptoms in adulthood.

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Year:  2007        PMID: 17235422     DOI: 10.1007/s00115-006-2237-1

Source DB:  PubMed          Journal:  Nervenarzt        ISSN: 0028-2804            Impact factor:   1.214


  15 in total

1.  Central core disease is due to RYR1 mutations in more than 90% of patients.

Authors:  Shiwen Wu; M Carlos A Ibarra; May Christine V Malicdan; Kumiko Murayama; Yasuko Ichihara; Hirosato Kikuchi; Ikuya Nonaka; Satoru Noguchi; Yukiko K Hayashi; Ichizo Nishino
Journal:  Brain       Date:  2006-04-18       Impact factor: 13.501

2.  Central core disease-an investigation of a rare muscle cell abnormality.

Authors:  W K ENGEL; J B FOSTER; B P HUGHES; H E HUXLEY; R MAHLER
Journal:  Brain       Date:  1961-06       Impact factor: 13.501

3.  Oxidative enzymes and phosphorylase in central-core disease of muscle.

Authors:  V DUBOWITZ; A G PEARSE
Journal:  Lancet       Date:  1960-07-02       Impact factor: 79.321

4.  A new congenital non-progressive myopathy.

Authors:  K R MAGEE; G M SHY
Journal:  Brain       Date:  1956-12       Impact factor: 13.501

5.  [Central core disease with "structured cores" in type II-fibers (author's transl)].

Authors:  D Pongratz; M Heuser; C Koppenwallner; G Hübner
Journal:  Klin Wochenschr       Date:  1976-02-01

6.  Central core disease: ultrastructure of the sarcoplasmic reticulum and T-tubules.

Authors:  K Hayashi; R G Miller; A K Brownell
Journal:  Muscle Nerve       Date:  1989-02       Impact factor: 3.217

7.  [Clinical, histological and histochemical studies in a case of central core disease (central fibrillar myopathy)].

Authors:  F Mittelbach; D Pongratz
Journal:  Dtsch Z Nervenheilkd       Date:  1968

8.  Central core disease or not? Observations on a family with a non-progressive myopathy.

Authors:  J A Morgan-Hughes; E M Brett; B D Lake; F M Tomé
Journal:  Brain       Date:  1973-09       Impact factor: 13.501

9.  Observations on central core disease.

Authors:  J Bethlem; G K van Wijngaarden; A E Meijer; P Fleury
Journal:  J Neurol Sci       Date:  1971-11       Impact factor: 3.181

10.  Central core disease of muscle with focal wasting.

Authors:  V Dubowitz; M Platts
Journal:  J Neurol Neurosurg Psychiatry       Date:  1965-10       Impact factor: 10.154

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  1 in total

1.  Core Disease in an Adult.

Authors:  Ashmeet Kaur; Kusum Mathur; Anita Harsh
Journal:  Ann Indian Acad Neurol       Date:  2022-07-14       Impact factor: 1.714

  1 in total

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