Literature DB >> 17200249

XXY (Klinefelter syndrome): a pediatric quantitative brain magnetic resonance imaging case-control study.

Jay N Giedd1, Liv S Clasen, Gregory L Wallace, Rhoshel K Lenroot, Jason P Lerch, Elizabeth Molloy Wells, Jonathan D Blumenthal, Jean E Nelson, Julia W Tossell, Catherine Stayer, Alan C Evans, Carole A Samango-Sprouse.   

Abstract

OBJECTIVE: An extra X chromosome in males (XXY), known as Klinefelter syndrome, is associated with characteristic physical, cognitive, and behavioral features of variable severity. The objective of this study was to examine possible neuroanatomical substrates of these cognitive and behavioral features during childhood and adolescence.
METHODS: MRI brain scans were acquired for 42 XXY and 87 healthy XY age-matched control males. We compared these 2 groups on regional brain volumes and cortical thickness.
RESULTS: Total cerebral volume and all lobar volumes except parietal white matter were significantly smaller in the XXY group, whereas lateral-ventricle volume was larger. Consistent with the cognitive profile, the cortex was significantly thinner in the XXY group in left inferior frontal, temporal, and superior motor regions.
CONCLUSION: The brain-imaging findings of preferentially affected frontal, temporal, and motor regions and relative sparing of parietal regions are consistent with observed cognitive and behavioral strengths and weaknesses in XXY subjects.

Entities:  

Mesh:

Year:  2007        PMID: 17200249     DOI: 10.1542/peds.2005-2969

Source DB:  PubMed          Journal:  Pediatrics        ISSN: 0031-4005            Impact factor:   7.124


  44 in total

1.  Increased medial temporal lobe and striatal grey-matter volume in a rare disorder of androgen excess: a voxel-based morphometry (VBM) study.

Authors:  Sven C Mueller; Deborah P Merke; Ellen W Leschek; Steven Fromm; Carol VanRyzin; Monique Ernst
Journal:  Int J Neuropsychopharmacol       Date:  2010-09-22       Impact factor: 5.176

Review 2.  Structural and functional neuroimaging in Klinefelter (47,XXY) syndrome: a review of the literature and preliminary results from a functional magnetic resonance imaging study of language.

Authors:  Kyle Steinman; Judith Ross; Song Lai; Allan Reiss; Fumiko Hoeft
Journal:  Dev Disabil Res Rev       Date:  2009

3.  Executive function in young males with Klinefelter (XXY) syndrome with and without comorbid attention-deficit/hyperactivity disorder.

Authors:  Nancy Raitano Lee; Gregory L Wallace; Liv S Clasen; Rhoshel K Lenroot; Jonathan D Blumenthal; Samantha L White; Mark J Celano; Jay N Giedd
Journal:  J Int Neuropsychol Soc       Date:  2011-05       Impact factor: 2.892

4.  Allometric Analysis Detects Brain Size-Independent Effects of Sex and Sex Chromosome Complement on Human Cerebellar Organization.

Authors:  Catherine Mankiw; Min Tae M Park; P K Reardon; Ari M Fish; Liv S Clasen; Deanna Greenstein; Jay N Giedd; Jonathan D Blumenthal; Jason P Lerch; M Mallar Chakravarty; Armin Raznahan
Journal:  J Neurosci       Date:  2017-03-17       Impact factor: 6.167

5.  Common functional polymorphisms of DISC1 and cortical maturation in typically developing children and adolescents.

Authors:  A Raznahan; Y Lee; R Long; D Greenstein; L Clasen; A Addington; J L Rapoport; J N Giedd
Journal:  Mol Psychiatry       Date:  2010-07-13       Impact factor: 15.992

6.  Neural systems for social cognition in Klinefelter syndrome (47,XXY): evidence from fMRI.

Authors:  Sophie van Rijn; Hanna Swaab; Daan Baas; Edward de Haan; René S Kahn; André Aleman
Journal:  Soc Cogn Affect Neurosci       Date:  2011-07-06       Impact factor: 3.436

7.  Dosage effects of X and Y chromosomes on language and social functioning in children with supernumerary sex chromosome aneuploidies: implications for idiopathic language impairment and autism spectrum disorders.

Authors:  Nancy Raitano Lee; Gregory L Wallace; Elizabeth I Adeyemi; Katherine C Lopez; Jonathan D Blumenthal; Liv S Clasen; Jay N Giedd
Journal:  J Child Psychol Psychiatry       Date:  2012-07-25       Impact factor: 8.982

Review 8.  Sex differences in cognitive impairment and Alzheimer's disease.

Authors:  Rena Li; Meharvan Singh
Journal:  Front Neuroendocrinol       Date:  2014-01-13       Impact factor: 8.606

Review 9.  Effects of sex chromosome aneuploidies on brain development: evidence from neuroimaging studies.

Authors:  Rhoshel K Lenroot; Nancy Raitano Lee; Jay N Giedd
Journal:  Dev Disabil Res Rev       Date:  2009

Review 10.  The cognitive phenotype in Klinefelter syndrome: a review of the literature including genetic and hormonal factors.

Authors:  Richard Boada; Jennifer Janusz; Christa Hutaff-Lee; Nicole Tartaglia
Journal:  Dev Disabil Res Rev       Date:  2009
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