Literature DB >> 17092782

Cystic fibrosis related diabetes in an extremely young patient.

Luis Casas1, Debbie R Berry, Kathy Logan, Kenneth C Copeland, James A Royall.   

Abstract

Diabetes in patients with cystic fibrosis (CF) is common but typically does not occur before the age of 10 years. We describe a male with cystic fibrosis who developed diabetes, consistent with cystic fibrosis related diabetes, at the age of 2 years and treated successfully with insulin.

Entities:  

Mesh:

Substances:

Year:  2006        PMID: 17092782     DOI: 10.1016/j.jcf.2006.08.004

Source DB:  PubMed          Journal:  J Cyst Fibros        ISSN: 1569-1993            Impact factor:   5.482


  5 in total

1.  A Transient Metabolic Recovery from Early Life Glucose Intolerance in Cystic Fibrosis Ferrets Occurs During Pancreatic Remodeling.

Authors:  Yaling Yi; Xingshen Sun; Katherine Gibson-Corley; Weiliang Xie; Bo Liang; Nan He; Scott R Tyler; Aliye Uc; Louis H Philipson; Kai Wang; Manami Hara; Katie Larson Ode; Andrew W Norris; John F Engelhardt
Journal:  Endocrinology       Date:  2016-02-10       Impact factor: 4.736

Review 2.  Epidemiology, pathophysiology, and prognostic implications of cystic fibrosis-related diabetes: a technical review.

Authors:  Antoinette Moran; Dorothy Becker; Samuel J Casella; Peter A Gottlieb; M Sue Kirkman; Bruce C Marshall; Bonnie Slovis
Journal:  Diabetes Care       Date:  2010-12       Impact factor: 19.112

3.  Structural abnormalities in islets from very young children with cystic fibrosis may contribute to cystic fibrosis-related diabetes.

Authors:  Marika Bogdani; Scott M Blackman; Cecilia Ridaura; Jean-Pierre Bellocq; Alvin C Powers; Lydia Aguilar-Bryan
Journal:  Sci Rep       Date:  2017-12-08       Impact factor: 4.379

4.  Long-Term Follow-Up in a Girl with Cystic Fibrosis and Diabetes Since the First Year of Life.

Authors:  Valentina Fattorusso; Alida Casale; Valeria Raia; Enza Mozzillo; Adriana Franzese
Journal:  Diabetes Ther       Date:  2017-08-02       Impact factor: 2.945

5.  Short-term CFTR inhibition reduces islet area in C57BL/6 mice.

Authors:  Dawood Khan; Ryan Kelsey; Rashmi R Maheshwari; Virginia M Stone; Annie Hasib; Fiona N Manderson Koivula; Aoife Watson; Stephen Harkin; Nigel Irwin; James A Shaw; Neville H McClenaghan; Viktória Venglovecz; Attila Ébert; Malin Flodström-Tullberg; Michael G White; Catriona Kelly
Journal:  Sci Rep       Date:  2019-08-02       Impact factor: 4.379

  5 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.