BACKGROUND: Although esophageal strictures caused by epidermolysis bullosa are often treated with balloon dilations, complete obstruction has few effective therapies except esophagectomy with colonic replacement. OBJECTIVE: Resolution of esophageal obstructive lesion without surgical intervention. DESIGN: Case study. SETTING: Interventional radiology. PATIENT: Epidermolysis bullosa with esophageal stricture. INTERVENTION: Endoscopic- and guidewire-guided sharp recanalization. MAIN OUTCOME MEASUREMENT: Radiologic evidence of stricture resolution. RESULTS: Successful recanalization. LIMITATIONS: Experience of operators (anesthesiologist, endoscopist, interventional radiologist). CONCLUSIONS: Sharp recanalization of a complete stricture in patients with epidermolysis bullosa is feasible in a controlled setting.
BACKGROUND: Although esophageal strictures caused by epidermolysis bullosa are often treated with balloon dilations, complete obstruction has few effective therapies except esophagectomy with colonic replacement. OBJECTIVE: Resolution of esophageal obstructive lesion without surgical intervention. DESIGN: Case study. SETTING: Interventional radiology. PATIENT: Epidermolysis bullosa with esophageal stricture. INTERVENTION: Endoscopic- and guidewire-guided sharp recanalization. MAIN OUTCOME MEASUREMENT: Radiologic evidence of stricture resolution. RESULTS: Successful recanalization. LIMITATIONS: Experience of operators (anesthesiologist, endoscopist, interventional radiologist). CONCLUSIONS: Sharp recanalization of a complete stricture in patients with epidermolysis bullosa is feasible in a controlled setting.