Literature DB >> 17041381

Successful treatment of idiopathic febrile panniculitis (Weber-Christian disease) with thalidomide in a patient having failed multiple other medical therapies.

H Richard Barthel1, Ulrich Charrier, Martin Kramer, Christoph Loch.   

Abstract

The authors describe a case of idiopathic nodular panniculitis (Weber-Christian disease) with recurrent febrile episodes resistant to glucocorticosteroids and methotrexate (MTX) in various combinations with hydroxychloroquine, azathioprine, cyclosporine, colchicine, and doxycycline. Thalidomide at 100 mg/day has induced a remission for 3 years.

Entities:  

Year:  2002        PMID: 17041381     DOI: 10.1097/00124743-200210000-00005

Source DB:  PubMed          Journal:  J Clin Rheumatol        ISSN: 1076-1608            Impact factor:   3.517


  2 in total

1.  Weber-Christian disease with ileocolonic involvement successfully treated with infliximab.

Authors:  José Miranda-Bautista; Alejandro Fernández-Simón; Isabel Pérez-Sánchez; Luis Menchén
Journal:  World J Gastroenterol       Date:  2015-05-07       Impact factor: 5.742

2.  Efficacy of cyclosporine A treatment in relapsing febrile lobular panniculitis associated with small vessel vasculitis.

Authors:  Luca Cantarini; Francesca Fanti; Mauro Galeazzi; Silvana Martino; Clelia Miracco; Maurizio Biagioli; Norberto Dal Canto; Rolando Cimaz
Journal:  Rheumatol Int       Date:  2009-06-09       Impact factor: 2.631

  2 in total

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