Literature DB >> 16969315

[Churg-Strauss syndrome and pulmonary fibrosis: an unusual association].

Maté Streho1, Régis Sable-Fourtassou, Marie Charlotte Brion, Isabelle Bourotte, Dominique Valeyre, Michel Brauner, Robin Dhote, Sébastien Abad.   

Abstract

INTRODUCTION: Churg-Strauss syndrome (CSS) is characterized by asthma, hypereosinophilia, and vasculitis involving at least two extrapulmonary organs. CASE: We report a case of a patient with antineutrophilic cytoplasmic antibody-negative CSS who developed pulmonary interstitial fibrosis (PIF). DISCUSSION: The possible relations between CSS and PIF are discussed. Because this case report is the first to describe features of pulmonary fibrosis in a patient with CSS, we cannot know whether this association is causal or fortuitous.

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Year:  2006        PMID: 16969315     DOI: 10.1016/s0755-4982(06)74799-6

Source DB:  PubMed          Journal:  Presse Med        ISSN: 0755-4982            Impact factor:   1.228


  3 in total

Review 1.  Interstital lung disease in ANCA vasculitis.

Authors:  Marco A Alba; Luis Felipe Flores-Suárez; Ashley G Henderson; Hong Xiao; Peiqi Hu; Patrick H Nachman; Ronald J Falk; J Charles Jennette
Journal:  Autoimmun Rev       Date:  2017-05-04       Impact factor: 9.754

2.  Eosinophilic Granulomatosis with Polyangiitis (EGPA) and Hepatitis B Infection - A Rare Association.

Authors:  Nidhi Kaeley; Narula Kamakshi
Journal:  J Clin Diagn Res       Date:  2016-12-01

Review 3.  Pulmonary fibrosis in antineutrophil cytoplasmic antibodies (ANCA)-associated vasculitis: a series of 49 patients and review of the literature.

Authors:  Cloé Comarmond; Bruno Crestani; Abdellatif Tazi; Baptiste Hervier; Sylvain Adam-Marchand; Hilario Nunes; Fleur Cohen-Aubart; Marie Wislez; Jacques Cadranel; Bruno Housset; Célia Lloret-Linares; Pascal Sève; Christian Pagnoux; Sébastien Abad; Juliette Camuset; Boris Bienvenu; Michaël Duruisseaux; Eric Hachulla; Jean-Benoît Arlet; Mohammed Hamidou; Alfred Mahr; Matthieu Resche-Rigon; Anne-Laure Brun; Philippe Grenier; Patrice Cacoub; David Saadoun
Journal:  Medicine (Baltimore)       Date:  2014-11       Impact factor: 1.889

  3 in total

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