A rare tumor located in the anorectal junction: sarcomatoid carcinoma.

Sarcomatoid carcinoma is a very rare tumor. Though it has been more than a century since sarcomatoid carcinoma was first described by Wirchow, many unresolved points remain. Histogenesis and nomenclature are controversial. A proper management has not been defined. Patients suffering from this aggressive tumor have a very poor prognosis. However, in this paper a case with a disease-free survival of more than five years is reported.