Segmental defect of intestinal musculature: a rare cause of intestinal obstruction in children.

A 3 years old female child was brought to the emergency department with acute abdomen. Laparotomy disclosed multiple segmental dilatations in the middle third of the ileum which was resected and anastomosed. Post-operative recovery was uneventful. Histopathological findings showed lack of smooth and longitudinal muscles in dilated segments of the intestine with intact mucosa without any evidence of necrosis and inflammation.