Tricuspid atresia: current concepts in diagnosis and treatment.

Tricuspid atresia is the third most common cyanotic cardiac malformation, seen in 1 per cent of children with congenital heart disease. Anatomic details in each patient can be elucidated by echocardiography. Surgical treatment initially is palliation, usually with aortopulmonary shunt. Definitive treatment is with a Fontan operation, in which the systemic venous return is connected directly to the pulmonary arterial tree. Long-term results of the corrective procedure have been very good.