Literature DB >> 16894125

The MM2-cortical form of sporadic Creutzfeldt-Jakob disease presenting with visual disturbance.

I Nozaki1, T Hamaguchi, M Noguchi-Shinohara, K Ono, H Shirasaki, K Komai, T Kitamoto, M Yamada.   

Abstract

A subclass of sporadic Creutzfeldt-Jakob disease (sCJD) characterized by onset with visual symptoms (Heidenhain variant) has been reported to belong to the MM1 or MV1 type according to Parchi's classification. The authors report a 65-year-old woman with MM2-cortical sCJD with slowly progressive visual disturbance as the initial symptom. Diffusion-weighted MRIs revealed hyperintensity in both occipital cortices at an early stage.

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Year:  2006        PMID: 16894125     DOI: 10.1212/01.wnl.0000228224.35678.60

Source DB:  PubMed          Journal:  Neurology        ISSN: 0028-3878            Impact factor:   9.910


  7 in total

1.  MRI abnormalities found 1 year prior to symptom onset in a case of Creutzfeldt-Jakob disease.

Authors:  Federico Verde; Nicola Ticozzi; Stefano Messina; Narghes Calcagno; Floriano Girotti; Luca Maderna; Fabio Moda; Elisa Scola; Andrea Falini; Fabrizio Tagliavini; Vincenzo Silani
Journal:  J Neurol       Date:  2016-02-12       Impact factor: 4.849

2.  Co-occurrence of types 1 and 2 PrP(res) in sporadic Creutzfeldt-Jakob disease MM1.

Authors:  Atsushi Kobayashi; Kenta Mizukoshi; Yasushi Iwasaki; Hajime Miyata; Yasuji Yoshida; Tetsuyuki Kitamoto
Journal:  Am J Pathol       Date:  2011-03       Impact factor: 4.307

Review 3.  Distinguishing Neuroimaging Features in Patients Presenting with Visual Hallucinations.

Authors:  T T Winton-Brown; A Ting; R Mocellin; M Walterfang; D Velakoulis; F Gaillard
Journal:  AJNR Am J Neuroradiol       Date:  2016-01-07       Impact factor: 3.825

4.  Revisiting the Heidenhain Variant of Creutzfeldt-Jakob Disease: Evidence for Prion Type Variability Influencing Clinical Course and Laboratory Findings.

Authors:  Simone Baiardi; Sabina Capellari; Anna Ladogana; Silvia Strumia; Mario Santangelo; Maurizio Pocchiari; Piero Parchi
Journal:  J Alzheimers Dis       Date:  2016       Impact factor: 4.472

5.  Clinicopathological findings of an MM2-cortical-type sporadic Creutzfeldt-Jakob disease patient with cortical blindness during a course of glaucoma and age-related macular degeneration.

Authors:  Yuichi Hayashi; Yasushi Iwasaki; Masahiro Waza; Hideaki Shibata; Akio Akagi; Akio Kimura; Takashi Inuzuka; Katsuya Satoh; Tetsuyuki Kitamoto; Mari Yoshida; Takayoshi Shimohata
Journal:  Prion       Date:  2019-01       Impact factor: 3.931

6.  Characterization of Sporadic Creutzfeldt-Jakob Disease and History of Neurosurgery to Identify Potential Iatrogenic Cases.

Authors:  Tsuyoshi Hamaguchi; Kenji Sakai; Atsushi Kobayashi; Tetsuyuki Kitamoto; Ryusuke Ae; Yosikazu Nakamura; Nobuo Sanjo; Kimihito Arai; Mizuho Koide; Fumiaki Katada; Masafumi Harada; Hiroyuki Murai; Shigeo Murayama; Tadashi Tsukamoto; Hidehiro Mizusawa; Masahito Yamada
Journal:  Emerg Infect Dis       Date:  2020-06       Impact factor: 6.883

7.  Agraphia of Kanji (Chinese characters): an early symptom of sporadic Creutzfeldt-Jakob disease in a Japanese patient: a case report.

Authors:  Keiko Nakamura; Kenji Sakai; Miharu Samuraki; Ichiro Nozaki; Masako Notoya; Masahito Yamada
Journal:  J Med Case Rep       Date:  2014-08-06
  7 in total

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