Literature DB >> 16870879

Lysine intake and neurotoxicity in glutaric aciduria type I: towards a rationale for therapy?

Stefan Kölker, Sven W Sauer, Jürgen G Okun, Georg F Hoffmann, David M Koeller.   

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Year:  2006        PMID： 16870879     DOI： 10.1093/brain/awl137

Source DB:  PubMed          Journal:  Brain        ISSN： 0006-8950            Impact factor:   13.501


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  10 in total

1.  Increased serum levels of L-arginine in ulcerative colitis and correlation with disease severity.

Authors:  Shih-Kuang S Hong; Brad E Maltz; Lori A Coburn; James C Slaughter; Rupesh Chaturvedi; David A Schwartz; Keith T Wilson
Journal:  Inflamm Bowel Dis       Date:  2010-01       Impact factor: 5.325

2.  Toxic Synergism Between Quinolinic Acid and Glutaric Acid in Neuronal Cells Is Mediated by Oxidative Stress: Insights to a New Toxic Model.

Authors:  Paula Pierozan; Ana Laura Colín-González; Helena Biasibetti; Janaina Camacho da Silva; Angela Wyse; Moacir Wajner; Abel Santamaria
Journal:  Mol Neurobiol       Date:  2017-09-21       Impact factor: 5.590

3.  Disturbance of Mitochondrial Dynamics, Endoplasmic Reticulum-Mitochondria Crosstalk, Redox Homeostasis, and Inflammatory Response in the Brain of Glutaryl-CoA Dehydrogenase-Deficient Mice: Neuroprotective Effects of Bezafibrate.

Authors:  Bianca Seminotti; Morgana Brondani; Rafael Teixeira Ribeiro; Guilhian Leipnitz; Moacir Wajner
Journal:  Mol Neurobiol       Date:  2022-05-31       Impact factor: 5.682

4.  Oxidative Stress, Disrupted Energy Metabolism, and Altered Signaling Pathways in Glutaryl-CoA Dehydrogenase Knockout Mice: Potential Implications of Quinolinic Acid Toxicity in the Neuropathology of Glutaric Acidemia Type I.

Authors:  Bianca Seminotti; Alexandre Umpierrez Amaral; Rafael Teixeira Ribeiro; Marília Danyelle Nunes Rodrigues; Ana Laura Colín-González; Guilhian Leipnitz; Abel Santamaría; Moacir Wajner
Journal:  Mol Neurobiol       Date:  2015-11-25       Impact factor: 5.590

5.  Higher Vulnerability of Menadione-Exposed Cortical Astrocytes of Glutaryl-CoA Dehydrogenase Deficient Mice to Oxidative Stress, Mitochondrial Dysfunction, and Cell Death: Implications for the Neurodegeneration in Glutaric Aciduria Type I.

Authors:  Marília Danyelle Nunes Rodrigues; Bianca Seminotti; Ângela Zanatta; Aline de Mello Gonçalves; Bruna Bellaver; Alexandre Umpierrez Amaral; André Quincozes-Santos; Stephen Irwin Goodman; Michael Woontner; Diogo Onofre Souza; Moacir Wajner
Journal:  Mol Neurobiol       Date:  2016-08-10       Impact factor: 5.590

Review 6.  Neurodegeneration and chronic renal failure in methylmalonic aciduria--a pathophysiological approach.

Authors:  M A Morath; J G Okun; I B Müller; S W Sauer; F Hörster; G F Hoffmann; S Kölker
Journal:  J Inherit Metab Dis       Date:  2007-09-12       Impact factor: 4.982

7.  Effects of targeted suppression of glutaryl-CoA dehydrogenase by lentivirus-mediated shRNA and excessive intake of lysine on apoptosis in rat striatal neurons.

Authors:  Jinzhi Gao; Cai Zhang; Xi Fu; Qin Yi; Fengyan Tian; Qin Ning; Xiaoping Luo
Journal:  PLoS One       Date:  2013-05-02       Impact factor: 3.240

8.  N-acetylcysteine prevents spatial memory impairment induced by chronic early postnatal glutaric acid and lipopolysaccharide in rat pups.

Authors:  Fernanda S Rodrigues; Mauren A Souza; Danieli V Magni; Ana Paula O Ferreira; Bibiana C Mota; Andreia M Cardoso; Mariana Paim; Léder L Xavier; Juliano Ferreira; Maria Rosa C Schetinger; Jaderson C Da Costa; Luiz Fernando F Royes; Michele R Fighera
Journal:  PLoS One       Date:  2013-10-24       Impact factor: 3.240

Review 9.  Single amino acid supplementation in aminoacidopathies: a systematic review.

Authors:  Danique van Vliet; Terry G J Derks; Margreet van Rijn; Martijn J de Groot; Anita MacDonald; M Rebecca Heiner-Fokkema; Francjan J van Spronsen
Journal:  Orphanet J Rare Dis       Date:  2014-01-13       Impact factor: 4.123

Review 10.  Nuclear Factor Erythroid-2-Related Factor 2 Signaling in the Neuropathophysiology of Inherited Metabolic Disorders.

Authors:  Bianca Seminotti; Mateus Grings; Paolo Tucci; Guilhian Leipnitz; Luciano Saso
Journal:  Front Cell Neurosci       Date:  2021-11-26       Impact factor: 5.505
  10 in total

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