Literature DB >> 16767559

A case of systemic sclerosis complicated by idiopathic portal hypertension: case report and literature review.

Kenji Takagi1, Shinichiro Nishio, Kimiko Akimoto, Takumi Yoshino, Shinichi Kawai.   

Abstract

We encountered a 62-year-old woman who had systemic sclerosis (SSc) complicated by idiopathic portal hypertension (IPH). She had a 10-year history of scleroderma and Raynaud's phenomenon. She also had pancytopenia, splenomegaly, and esophageal varices. Treatment with prednisolone and endoscopic variceal ligation resulted in improvement of her symptoms. According to our literature review, the prognosis of patients with SSc complicated by IPH is relatively poor. However, the factors that predict outcome of these patients have not been elucidated.

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Year:  2006        PMID: 16767559     DOI: 10.1007/s10165-006-0479-1

Source DB:  PubMed          Journal:  Mod Rheumatol        ISSN: 1439-7595            Impact factor:   3.023


  5 in total

Review 1.  Clinical characteristics of idiopathic portal hypertension.

Authors:  Ozgur Harmanci; Yusuf Bayraktar
Journal:  World J Gastroenterol       Date:  2007-04-07       Impact factor: 5.742

2.  Is spleen circulation impaired in systemic sclerosis and what is the role of liver fibrosis?

Authors:  Giovanni Tarantino; Angelo Spanò; Gabriella Loi; Anna Parisi; Marianna Tarantino; Giuseppina Brancaccio; Giovanni Battista Gaeta; Antonio Riccio
Journal:  World J Gastroenterol       Date:  2011-03-28       Impact factor: 5.742

3.  Life-threatening hypersplenism due to idiopathic portal hypertension in early childhood: case report and review of the literature.

Authors:  Jan Däbritz; Jennifer Worch; Ulrike Materna; Bernward Koch; Gabriele Koehler; Christina Duck; Michael C Frühwald; Dirk Foell
Journal:  BMC Gastroenterol       Date:  2010-10-20       Impact factor: 3.067

4.  Analysis of inherited thrombophilic mutations and natural anticoagulant deficiency in patients with idiopathic portal hypertension.

Authors:  Kadim Bayan; Yekta Tüzün; Serif Yilmaz; Naime Canoruc; Mehmet Dursun
Journal:  J Thromb Thrombolysis       Date:  2008-08-07       Impact factor: 2.300

5.  Imaging and Pathological Features of Idiopathic Portal Hypertension and Differential Diagnosis from Liver Cirrhosis.

Authors:  Zhen-Long Zhao; Ying Wei; Tai-Ling Wang; Li-Li Peng; Yan Li; Ming-An Yu
Journal:  Sci Rep       Date:  2020-02-12       Impact factor: 4.379

  5 in total

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