Literature DB >> 16675853

C. elegans as a model for Friedreich Ataxia.

Natascia Ventura, Shane L Rea, Samuel T Handerson, Ivano Condò, Roberto Testi, Thomas E Johnson.   

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Year:  2006        PMID: 16675853     DOI: 10.1096/fj.06-0505ufm

Source DB:  PubMed          Journal:  FASEB J        ISSN: 0892-6638            Impact factor:   5.191


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  6 in total

1.  Paradigm for disease deconvolution in rare neurodegenerative disorders in Indian population: insights from studies in cerebellar ataxias.

Authors:  Renu Kumari; Deepak Kumar; Samir K Brahmachari; Achal K Srivastava; Mohammed Faruq; Mitali Mukerji
Journal:  J Genet       Date:  2018-07       Impact factor: 1.166

2.  Mapping iron binding sites on human frataxin: implications for cluster assembly on the ISU Fe-S cluster scaffold protein.

Authors:  Jia Huang; Eric Dizin; J A Cowan
Journal:  J Biol Inorg Chem       Date:  2008-04-19       Impact factor: 3.358

3.  Relationship between mitochondrial electron transport chain dysfunction, development, and life extension in Caenorhabditis elegans.

Authors:  Shane L Rea; Natascia Ventura; Thomas E Johnson
Journal:  PLoS Biol       Date:  2007-10-02       Impact factor: 8.029

4.  Time-resolved functional analysis of acute impairment of frataxin expression in an inducible cell model of Friedreich ataxia.

Authors:  Dörte Poburski; Josefine Barbara Boerner; Michel Koenig; Michael Ristow; René Thierbach
Journal:  Biol Open       Date:  2016-05-15       Impact factor: 2.422

5.  Autophagy induction extends lifespan and reduces lipid content in response to frataxin silencing in C. elegans.

Authors:  Alfonso Schiavi; Alessandro Torgovnick; Alison Kell; Evgenia Megalou; Natascha Castelein; Ilaria Guccini; Laura Marzocchella; Sara Gelino; Malene Hansen; Florence Malisan; Ivano Condò; Roberto Bei; Shane L Rea; Bart P Braeckman; Nektarios Tavernarakis; Roberto Testi; Natascia Ventura
Journal:  Exp Gerontol       Date:  2012-12-13       Impact factor: 4.032

6.  HDAC inhibitors correct frataxin deficiency in a Friedreich ataxia mouse model.

Authors:  Myriam Rai; Elisabetta Soragni; Kai Jenssen; Ryan Burnett; David Herman; Giovanni Coppola; Daniel H Geschwind; Joel M Gottesfeld; Massimo Pandolfo
Journal:  PLoS One       Date:  2008-04-09       Impact factor: 3.240

  6 in total

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