Literature DB >> 16639628

Aplasia cutis congenita of the scalp: is there a better treatment strategy?

Ricardo Santos de Oliveira1, Carlos Eduardo Barros Jucá, Antônio Lopes Lins-Neto, Maria Aparecida do Carmo Rego, Jaime Farina, Helio Rubens Machado.   

Abstract

BACKGROUND: Aplasia cutis congenita (ACC) is a rare disease of unknown etiology, involving any site of the body. The scalp is the most frequent location, followed by the forearms, knees, both sides of the trunk, and neck, in decreasing order of frequency. Superficial lesions may heal spontaneously and seldom result in morbidity or mortality. However, in patients with large scalp and skull defects, there are risks of infection and bleeding. Conservative treatment has been described and advocated, but some authors have highlighted the disadvantages of this treatment modality. On the other hand, several authors claim that aggressive surgical treatment has an important role for large defects.
MATERIALS AND METHODS: In this paper, we report three newborns with ACC of the scalp, two large defects and a medium one, respectively, treated conservatively and surgically.
CONCLUSION: The management of ACC of the scalp is still controversial. Our series suggests that conservative treatment should be performed for initial management in newborns.

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Year:  2006        PMID: 16639628     DOI: 10.1007/s00381-006-0074-y

Source DB:  PubMed          Journal:  Childs Nerv Syst        ISSN: 0256-7040            Impact factor:   1.475


  37 in total

1.  Aplasia cutis congenita of the scalp: excessive bleeding and reconstructive problems.

Authors:  K Islamoglu; E Ozgentas
Journal:  Ann Plast Surg       Date:  2001-08       Impact factor: 1.539

2.  Cutis aplasia.

Authors:  C S Smit; B J Zeeman
Journal:  Plast Reconstr Surg       Date:  1992-08       Impact factor: 4.730

3.  Repair of a congenital cranial defect in a newborn with autologous calvarial bone.

Authors:  P Steinbok
Journal:  Childs Nerv Syst       Date:  2000-04       Impact factor: 1.475

4.  Congenital defects of the scalp. A surgical approach to aplasia cutis congenita.

Authors:  P J Lynch; E A Kahn
Journal:  J Neurosurg       Date:  1970-08       Impact factor: 5.115

Review 5.  Ventricular diverticulum at the posterior horn of the lateral ventricle presenting as aplasia cutis congenita.

Authors:  K Fujita; T Enomoto; K Yanaka; T Nose
Journal:  Childs Nerv Syst       Date:  2001-10-31       Impact factor: 1.475

6.  Polymicrogyria associated with scalp and limb defects: variant of Adams-Oliver syndrome.

Authors:  D J Amor; R J Leventer; S Hayllar; A Bankier
Journal:  Am J Med Genet       Date:  2000-08-14

7.  Aplasia cutis congenita of the scalp: delayed closure complicated by massive hemorrhage.

Authors:  D W Glasson; G M Duncan
Journal:  Plast Reconstr Surg       Date:  1985-03       Impact factor: 4.730

8.  Complete osseous regeneration of a large skull defect in a patient with cutis aplasia: a conservative approach.

Authors:  Samuel T Rhee; Christopher Colville; Steven R Buchman; K Muraszko
Journal:  J Craniofac Surg       Date:  2002-07       Impact factor: 1.046

9.  Leptomeningeal angiomatosis and aplasia congenita of the scalp. Case report.

Authors:  E Pozzati; R Padovani; F Frank; G Gaist
Journal:  J Neurosurg       Date:  1983-06       Impact factor: 5.115

10.  Vascular abnormalities in Adams-Oliver syndrome: cause or effect?

Authors:  E N Swartz; S Sanatani; G G Sandor; R A Schreiber
Journal:  Am J Med Genet       Date:  1999-01-01
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  7 in total

1.  Parental allografts in the management of Adams-Oliver syndrome.

Authors:  Tom O W Henderson; Gregory P L Thomas; Steven A Wall
Journal:  Childs Nerv Syst       Date:  2013-06-06       Impact factor: 1.475

2.  Dilemmas and challenges in the management of a neonate with Adams-Oliver syndrome with infected giant aplasia cutis lesion and exsanguination: a case-based update.

Authors:  Suhas Udayakumaran; Jimmy Mathew; Dilip Panikar
Journal:  Childs Nerv Syst       Date:  2012-12-29       Impact factor: 1.475

Review 3.  A practical approach to the evaluation and treatment of an infant with aplasia cutis congenita.

Authors:  S R Humphrey; X Hu; K Adamson; A Schaus; J N Jensen; B Drolet
Journal:  J Perinatol       Date:  2017-10-19       Impact factor: 2.521

Review 4.  Fatal superior sagittal sinus hemorrhage as a complication of aplasia cutis congenita: a case report and literature review.

Authors:  Rowena Johnson; Amaka Offiah; Marta C Cohen
Journal:  Forensic Sci Med Pathol       Date:  2015-01-23       Impact factor: 2.007

5.  Two different management modalities in a two sibling case report of Adams Oliver syndrome.

Authors:  Nada Al-Hadithy; Joanna Mennie; Ken Stewart
Journal:  BMJ Case Rep       Date:  2011-12-21

6.  Aplasia cutis congenita: Two case reports and discussion of the literature.

Authors:  Alexandros Blionas; Dimitrios Giakoumettis; Elias Antoniades; Evangelos Drosos; Andreas Mitsios; Sotirios Plakas; Georgios Sfakianos; Marios S Themistocleous
Journal:  Surg Neurol Int       Date:  2017-11-09

7.  Conservative Healing of an 11 × 9-cm Aplasia Cutis Congenita of the Scalp with Bone Defect.

Authors:  Victoria Fröjd; Giovanni Maltese; Lars Kölby; Peter Tarnow
Journal:  J Neurol Surg Rep       Date:  2014-08-11
  7 in total

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