| Literature DB >> 16627225 |
Akihiro Hosaka1, Tetsuro Miyata, Hiroshi Shigematsu, Jun-o Deguchi, Hideo Kimura, Hirokazu Nagawa, Osamu Sato, Takehiko Sakimoto, Tomoyuki Mochizuki.
Abstract
The vascular type of Ehlers-Danlos syndrome is a genetic disorder of connective tissue and is frequently associated with catastrophic arterial complications. Its surgical treatment is extremely difficult because of the fragility of vessels. This article describes three patients with vascular type of Ehlers-Danlos syndrome who developed mesenteric hemorrhage due to spontaneous arterial rupture. The clinical and molecular characteristics of the disease are briefly reviewed.Entities:
Mesh:
Year: 2006 PMID: 16627225 DOI: 10.1016/j.gassur.2005.07.018
Source DB: PubMed Journal: J Gastrointest Surg ISSN: 1091-255X Impact factor: 3.452