| Literature DB >> 16562593 |
H L Claahsen-van der Grinten1, C A Hulsbergen-van de Kaa, B J Otten.
Abstract
We report a young girl who died in an Addisonian crisis due to previously undiagnosed congenital adrenal hyperplasia (CAH), in whom ovarian adrenal rest tissue was detected at postmortem histopathological examination. This is a very rare complication in female patients with CAH with only two previously reported cases.Entities:
Mesh:
Year: 2006 PMID: 16562593 DOI: 10.1515/jpem.2006.19.2.177
Source DB: PubMed Journal: J Pediatr Endocrinol Metab ISSN: 0334-018X Impact factor: 1.634